Primary Immunodeficiencies in Costa Rican Adults

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Brief Title

Primary Immunodeficiencies in Costa Rican Adults

Official Title

CASE SERIES OF PRIMARY IMMUNODEFICIENCIES IN ADULTS DIAGNOSED IN TWO HOSPITALS OF THE TERTIARY LEVEL OF CARE OF THE COSTA RICAN SOCIAL SECURITY Fund, 2017-2018

Brief Summary

      Primary immunodeficiencies represent a underdiagnosed group of rare diseases which if
      diagnosed well and in time can be treated in an efficient manner and prevent complications
      that may affect the quality of patients life in an severe manner. Neither in Costa Rica nor
      in Central America studies or national registries regarding the prevalence and
      characterization of primary immunodeficiencies in adult patients exist up to now. This study
      reflects for the first time the epidemiologic situation of primary immunodeficiencies in a
      Central American country, characterizing adult patients diagnosed with primary and idiopathic
      immune disorders treated in two specialized immunodeficiency clinics in Costa Rica.
    



Study Type

Observational [Patient Registry]


Primary Outcome

Clinical manifestations of all adult patients diagnosed with primary and idiopathic immune defects

Secondary Outcome

 characterization of immunodeficient patients

Condition

Primary Immune Deficiency in Adults



Publications

* Includes publications given by the data provider as well as publications identified by National Clinical Trials Identifier (NCT ID) in Medline.

Recruitment Information



Estimated Enrollment

137

Start Date

November 11, 2018

Completion Date

November 11, 2019

Primary Completion Date

November 11, 2019

Eligibility Criteria

        Inclusion Criteria:

          -  All patients from adult primary immunodeficiency clinics will be included.

        Exclusion Criteria:

          -  Patients with HIV

          -  Proven secondary immunodeficiencies.
      

Gender

All

Ages

12 Years - 100 Years

Accepts Healthy Volunteers

No

Contacts

, , 

Location Countries

Costa Rica

Location Countries

Costa Rica

Administrative Informations


NCT ID

NCT04963660

Organization ID

R017-SABI-00148.


Responsible Party

Sponsor

Study Sponsor

Caja Costarricense de Seguro Social


Study Sponsor

, , 


Verification Date

July 2021