Hydroa vacciniforme


A rare skin disorder characterized the development of crusting skin eruptions following exposure to the sun


* Malaise * Hyperthermia * Restlessness * Itching * Skin eruption


The development of lesions and their distribution suggest a causal relationship between HV and ultraviolet (UV) exposure, although the pathogenetic mechanism remains unknown.5 Ultraviolet A (UV-A) radiation is most often implicated. Two reports of HV in siblings have been documented, suggesting a genetic component to HV.6 Some cases have occurred in the setting of hematopoietic malignancy.