Bencze syndrome


A rare inherited condition characterized mainly by abnormal, asymmetrical facial bone growth and eye problems in some cases.


* Facial asymmetry * Amblyopia * Crossed eyes * Submucous cleft palate * Impaired vision


* Esotropia –Defined as convergent visual axes or “crossed” eyes –Amblyopia and monocular blindness usually manifests as esodeviation in 0–3-year-olds * Exotropia –Defined as divergent visual gaze –Amblyopia and monocular blindness usually manifest as exodeviation in children older than 4 years * Pseudostrabismus: In young children with wide-spaced eyes, flat nasal bridge, or prominent epicanthal folds, the patient may appear to be esotropic