Amelogenesis Imperfecta hypomaturation type


Amelogenesis Imperfecta hypomaturation type (AIH) (medical condition) is subtype of Amelogenesis Imperfecta. Amelogenesis imperfecta is an inherited tooth development disorder characterized by tooth enamel defects. The hypomaturation type involves an abnormality during the maturation stage of enamel formation which causes the enamel to become porous and opaque.

In Amelogenesis Imperfecta hypomaturation type Varies from creamy opaque to marked yellow/brown, surface of teeth soft and rough, dental sensitivity and open bite common. In this type normal thickness with enamel that often chips and abrades easily. Also, the Enamel has contrast similar to or > than dentin, unerupted crowns have normal morphology. It is inherited autosomal dominant, recessive or X-linked.


  • Opaque tooth enamel
  • Porous tooth enamel


Genes responsible for hypomaturation AI (Type II) are tentatively assigned to the X chromosome and to locations on chromosome 19 and chromosome 11.


  • NIH