Disease: Spongiform encephalopathy
- "Prion-like" seeding and propagation of oligomeric protein assemblies in neurodegenerative disorders
- 18F-FDG PET/CT in early phase of sporadic Creutzfeldt-Jacob disease: A case report
- A discontinuous Galerkin method for the three-dimensional heterodimer model with application to prion-like proteins' dynamics
- A method for the analysis of the oligomerization profile of the Huntington's disease-associated, aggregation-prone mutant huntingtin protein by isopycnic ultracentrifugation
- A rare case of Sporadic Creutzfeldt-Jakob disease at a remote mountain hospital in the Indian Himalayan Region
- A review on the processing technique, physicochemical, and bioactive properties of marine collagen
- Adaptation of the protein misfolding cyclic amplification (PMCA) technique for the screening of anti-prion compounds
- Assessing freedom from chronic wasting disease in semi-domesticated reindeer in Norway and Sweden
- Assessment of the therapeutic potential of Hsp70 activator against prion diseases using in vitro and in vivo models
- Assessment of the Zoonotic Potential of Atypical Scrapie Prions in Humanized Mice Reveals Rare Phenotypic Convergence but Not Identity With Sporadic Creutzfeldt-Jakob Disease Prions
- Author Correction: Loss of TREM2 function increases amyloid seeding but reduces plaque-associated ApoE
- Biodetection of an odor signature in white-tailed deer associated with infection by chronic wasting disease prions
- Biological effects of sodium phenylbutyrate and taurursodiol in Alzheimer's disease
- Biophysical characterization of the phase separation of TDP-43 devoid of the C-terminal domain
- Brain perfusion SPECT in dementia: what radiologists should know
- Brainwide silencing of prion protein by AAV-mediated delivery of an engineered compact epigenetic editor
- Cell adhesion molecule CD44 is dispensable for reactive astrocyte activation during prion disease
- Cleavage site-directed antibodies reveal the prion protein in humans is shed by ADAM10 at Y226 and associates with misfolded protein deposits in neurodegenerative diseases
- Comparing Prion Proteins Across Species: Is Zebrafish a Useful Model?
- Construction of a prognostic model via WGCNA combined with the LASSO algorithm for stomach adenocarcinoma patients
- Convergent generation of atypical prions in knockin mouse models of genetic prion disease
- Creatine Promotes Endometriosis by Inducing Ferroptosis Resistance via Suppression of PrP
- Creutzfeldt-Jakob Disease and Fatal Familial Insomnia: Demographics and In-Hospital Mortality in Spain
- CWD as a New Health Threat in Europe and the Adequacy and Effectiveness of Instruments of Legal Response from a Comparative Legal Perspective
- Diagnosis of Hirschsprung disease by analyzing acetylcholinesterase staining using artificial intelligence
- Direct observation of prion-like propagation of protein misfolding templated by pathogenic mutants
- Distinct Imaging Markers of Leigh's Disease Linked to SURF1 Mutation: A Pediatric Case Study
- DNAJA2 and Hero11 mediate similar conformational extension and aggregation suppression of TDP-43
- Dysarthria as a Presenting Symptom With Rapidly Progressive Imaging Features in Sporadic Creutzfeldt-Jakob Disease: A Case Report
- Evaluating the Interaction of Emerging Diseases on White-Tailed Deer Populations Using an Agent-Based Modeling Approach
- Evaluation and Limitations of the Novel Chemiluminescent Enzyme Immunoassay Technique for Measuring Total Tau Protein in the Cerebrospinal Fluid of Patients with Human Prion Disease: A 10-Year Prospective Study (2011-2020)
- Expanding the Prion Paradigm to Include Alzheimer and Parkinson Diseases
- Exploring the genetic variability of the PRNP gene at codons 127, 142, 146, 154, 211, 222, and 240 in goats farmed in the Lombardy Region, Italy
- Extraneural infection route restricts prion conformational variability and attenuates the impact of quaternary structure on infectivity
- Fast-track neuropathological screening for neurodegenerative diseases
- First Report of Single Nucleotide Polymorphisms (SNPs) of the Leporine Shadow of Prion Protein Gene (SPRN) and Absence of Nonsynonymous SNPs in the Open Reading Frame (ORF) in Rabbits
- Fluid Biomarkers in Individuals at Risk for Genetic Prion Disease up to Disease Conversion
- Frontotemporal dementia-like disease progression elicited by seeded aggregation and spread of FUS
- GB applies for 'negligible risk' BSE status
- Genetic characterization of the prion protein gene in camels (Camelus) with comments on the evolutionary history of prion disease in Cetartiodactyla
- Genetic insights into drug targets for sporadic Creutzfeldt-Jakob disease: Integrative multi-omics analysis
- Genome wide association study of clinical duration and age at onset of sporadic CJD
- In silico analysis of fungal prion-like proteins for elucidating their role in plant-fungi interactions
- In situ seeding assay: A novel technique for direct tissue localization of bioactive tau
- Investigation of the inhibitory potential of caffeic acid phenethyl ester on prion replication, amplification, and fibril formation in vitro
- Lack of prion transmission barrier in human PrP transgenic Drosophila
- Longitudinal detection of prion infection in preclinical sheep blood samples compared using 3 assays
- Longitudinal microbiome investigation throughout prion disease course reveals pre- and symptomatic compositional perturbations linked to short-chain fatty acid metabolism and cognitive impairment in mice
- Magnetic resonance imaging pattern recognition of metabolic and neurodegenerative encephalopathies in dogs and cats
- MAVS Cys508 palmitoylation promotes its aggregation on the mitochondrial outer membrane and antiviral innate immunity
- Modulating the aggregation of human prion protein PrP(106-126) by an indole-based cyclometallated palladium complex
- Modulation of prion protein expression through cryptic splice site manipulation
- Neuropathologically directed profiling of PRNP somatic and germline variants in sporadic human prion disease
- Neuroprotective Effects of Curcumin in Neurodegenerative Diseases
- Norwegian moose CWD induces clinical disease and neuroinvasion in gene-targeted mice expressing cervid S138N prion protein
- Novel diagnostic and prognostic approach for rapidly progressive dementias: Indicators based on amyloid/tau/neurodegeneration (ATN) framework
- Outer membrane vesicles of <em>Acinetobacter baumannii</em> DS002 carry circular DNA similar to bovine meat and milk factors (BMMFs) and SPHINX 2.36 and probably play a role in interdomain lateral gene transfer
- Physiology of Cellular Prion Proteins in Reproduction
- Plasma extracellular vesicle tau and TDP-43 as diagnostic biomarkers in FTD and ALS
- Post-translational modifications in prion diseases
- Predicting chronic wasting disease in white-tailed deer at the county scale using machine learning
- Predicting Symptom Onset of Genetic Prion Diseases Using Fluid Biomarkers
- Prion diseases motor and neuropsychiatric symptom cluster pharmacotherapy: structured scoping review
- Prion diseases, always a threat?
- Prion protein E219K polymorphism: from the discovery of the KANNO blood group to interventions for human prion disease
- Prion protein gene (PRNP) variation in German and Danish cervids
- Prion Seeding Activity in Plant Tissues Detected by RT-QuIC
- Prion-like domain mediated phase separation of ARID1A promotes oncogenic potential of Ewing's sarcoma
- Propagation of distinct CWD prion strains during peripheral and intracerebral challenges of gene-targeted mice
- Proteases, a powerful biochemical tool in the service of medicine, clinical and pharmaceutical
- Rational design of structure-based vaccines targeting misfolded alpha-synuclein conformers of Parkinson's disease and related disorders
- Reactive astrocytes in prion diseases: Friend or foe?
- Research Priorities on the Role of α-Synuclein in Parkinson's Disease Pathogenesis
- Retention of prions in the polychaete <em>Hediste diversicolor</em> and black soldier fly, <em>Hermetia illucens</em>, larvae after short-term experimental immersion and feeding with brain homogenate from scrapie infected sheep
- Risk willingness in multiple system atrophy and Parkinson's disease understanding patient preferences
- RNA-Seq Analysis of Mammalian Prion Disease
- S100A9 inhibits and redirects prion protein 89-230 fragment amyloid aggregation
- Scrapie versus Chronic Wasting Disease in White-Tailed Deer
- Severe neurodegeneration in brains of transgenic rats producing human tau prions
- Silencing prion protein expression in the brain
- Simple 3D spheroid cell culture model for studies of prion infection
- Slow Misfolding of a Molten Globule form of a Mutant Prion Protein Variant into a beta-rich Dimer
- Structural Mapping of Protein Aggregates in Live Cells Modeling Huntington's Disease
- Structural Variations of Prions and Prion-like Proteins Associated with Neurodegeneration
- Syntaxin-6 delays prion protein fibril formation and prolongs presence of toxic aggregation intermediates
- Tau seeding activity in skin biopsy differentiates tauopathies from synucleinopathies
- Temporal and Spatial Clustering of Intracerebral Hemorrhage in Cerebral Amyloid Angiopathy
- The effect of Aβ seeding is dependent on the presence of knock-in genes in the <em>App</em> <sup><em>NL</em>-<em>G</em>-<em>F</em></sup> mice
- The First Genetic Characterization of the <em>SPRN</em> Gene in Pekin Ducks (<em>Anas platyrhynchos domesticus</em>)
- The Importance of Prion Research
- The prion-like effect and prion-like protein targeting strategy in amyotrophic lateral sclerosis
- The role of interferon beta in neurological diseases and its potential therapeutic relevance
- Towards multicenter β-amyloid PET imaging in mouse models: A triple scanner head-to-head comparison
- Transcriptome Analysis in Air-Liquid Interface Porcine Respiratory Epithelial Cell Cultures Reveals That the Betacoronavirus Porcine Encephalomyelitis Hemagglutinating Virus Induces a Robust Interferon Response to Infection
- Transmission of classical scrapie using lymph node inoculum
- Transmission of Norwegian reindeer CWD to sheep by intracerebral inoculation results in an unusual phenotype and prion distribution
- Understanding the molecular mechanisms of human diseases: the benefits of fission yeasts
- Unusually Late Onset of Creutzfeldt-Jakob Disease Following COVID-19 Infection in India: A Case Report
- Updated global epidemiology atlas of human prion diseases
- Whole-genome sequencing analysis reveals new susceptibility loci and structural variants associated with progressive supranuclear palsy
