• A Case of Primary Somatostatin-Producing Tumor of the Duodenum with Liver Metastases with Long-Term Survival of More than 20 Years
• A new twist in neuroendocrine tumor research: Pacak-Zhuang syndrome, HIF-2α as the major player in its pathogenesis and future therapeutic options
• A Rare Cause of a Subepithelial Periampullary Duodenal Lesion
• A short history of neuroendocrine tumours and their peptide hormones
• A Transgenic Mouse Model of Pacak⁻Zhuang Syndrome with An <em>Epas1</em> Gain-of-Function Mutation
• About secondary causes of diabetes mellitus
• An Insight on Functioning Pancreatic Neuroendocrine Neoplasms
• Analysis of Clinical Characteristics and Survival in Patients With Functional Neuroendocrine Tumors of Gastrointestinal Origin
• Biochemical markers for gastroenteropancreatic neuroendocrine tumours (GEP-NETs)
• C-Terminal, but Not Intact, FGF23 and EPO Are Strongly Correlatively Elevated in Patients With Gain-of-Function Mutations in HIF2A: Clinical Evidence for EPO Regulating FGF23
• Case report: recurrent acute pancreatitis secondary to papillary somatostatinoma--a new association
• Chiari Malformation Type 1 in <em>EPAS1</em>-Associated Syndrome
• Clinical Characteristics and Management of Functional Pancreatic Neuroendocrine Neoplasms: A Single Institution 20-Year Experience with 286 Patients
• Clinical features of pancreatic neuroendocrine tumors
• Clinical manifestations of Pacak-Zhuang syndrome in a male pediatric patient
• Clinical Presentation and Diagnosis of Pancreatic Neuroendocrine Tumors
• Clinicopathological Data and Treatment Modalities for Pancreatic Somatostatinomas
• Coexistence of neurofibromatosis type 1 with multiple malignant neoplasia
• Combined presence of multiple gastrointestinal stromal tumors along with duodenal submucosal somatostatinoma in a patient with neurofibromatosis type 1
• Comprehensive <em>in silico</em> and functional studies for classification of <em>EPAS1/HIF2A</em> genetic variants identified in patients with erythrocytosis
• Conditional c-MYC activation in catecholaminergic cells drives distinct neuroendocrine tumors: neuroblastoma vs somatostatinoma
• Correlative Light- and Electron Microscopy Using Quantum Dot Nanoparticles
• Cotargeting the PI3K and RAS pathways for the treatment of neuroendocrine tumors
• Course of Aggressive Somatotroph, Corticotroph and Mammotroph Tumors under Temozolomide; Report of Three Cases and Review of the Literature
• Developmental vascular malformations in EPAS1 gain-of-function syndrome
• Diabetes mellitus secondary to an endocrine pathology : when to think about it ?
• Diabetes Mellitus Secondary to Endocrine Diseases: An Update of Diagnostic and Treatment Particularities
• Diagnostic Management of Gastroenteropancreatic Neuroendocrine Neoplasms: Technique Optimization and Tips and Tricks for Radiologists
• Diarrhoea due to pancreatic diseases
• Differential diagnostic value of the expression of the transcription factor PDX-1 in neuroendocrine and non-neuroendocrine tumors of the pancreas and other organs
• Distinct mechanisms of hypoglycaemia in patients with somatostatin-secreting neuroendocrine tumours
• Duodenal somatostatinoma presenting as obstructive jaundice with the coexistence of a gastrointestinal stromal tumour in neurofibromatosis type 1: a case with review of the literature
• Duodenal somatostatinoma: a case report and review of the literature
• Education and imaging. Gastrointestinal: neurofibromatosis type 1, duodenal somatostatinoma and gastrointestinal stromal tumors; a triad worth remembering
• Endoscopic Ampullectomy of a Somatostatinoma
• Endoscopic ultrasound-guided fine-needle aspiration diagnosis of mixed endocrine somatostatinoma of the minor papilla in von Recklinghausen disease
• EPAS-1-related pheochromocytoma/paraganglioma: How common and how aggressive?
• EPAS1-related pheochromocytoma/paraganglioma
• European Neuroendocrine Tumor Society 2023 guidance paper for functioning pancreatic neuroendocrine tumour syndromes
• False-Negative Neuroendocrine Tumor Identified With 68 Ga-DOTATOC PET/CT : A Case of Well-Differentiated Somatostatinoma
• False-Negative Neuroendocrine Tumor Identified With 68Ga-DOTATOC PET/CT: A Case of Well-Differentiated Somatostatinoma
• Familial Duodenal Somatostatinomatosis Not Associated With a Known Genetic Syndrome
• First report of bilateral pheochromocytoma in the clinical spectrum of HIF2A-related polycythemia-paraganglioma syndrome
• Functional Imaging Signature of Patients Presenting with Polycythemia/Paraganglioma Syndromes
• Functional significance of germline EPAS1 variants
• Gastric somatostatinoma: an extremely rare cause of upper gastrointestinal bleeding
• HIF signaling pathway in pheochromocytoma and other neuroendocrine tumors
• HIF-2alpha: Achilles' heel of pseudohypoxic subtype paraganglioma and other related conditions
• Hypoxia-Inducible Factor 2α Mutation-Related Paragangliomas Classify as Discrete Pseudohypoxic Subcluster
• Imaging of Pancreatic-Neuroendocrine Tumours: An Outline of Conventional Radiological Techniques
• Incidence, hormonal distribution and postoperative follow up of atypical pituitary adenomas
• Influence of pretreatment with everolimus or sunitinib on the subacute hematotoxicity of ¹⁷⁷Lu-DOTATATE PRRT
• Infrequent presentation of neuroendocrine tumour: duodenal somatostatinoma
• Inherited tumor syndromes of gastroenteropancreatic and thoracic neuroendocrine neoplasms
• Involvement of the gamma1 subunit of the large-conductance Ca(2+)-activated K(+) channel in the proliferation of human somatostatinoma cells
• Involvement of the γ1 subunit of the large-conductance Ca²⁺-activated K⁺ channel in the proliferation of human somatostatinoma cells
• LONG-TERM FOLLOW-UP OF DUODENAL PAPILLARY SOMATOSTATINOMA TREATED BY ENDOSCOPIC PAPILLECTOMY
• Management of functional neuroendocrine tumors of the pancreas
• Mixed mucinous adenocarcinoma and somatostatinoma of the ampulla of Vater associated with neurofibromatosis type 1
• Mixed periampullary adenocarcinoma and somatostatinoma with small bowel gastrointestinal stromal tumour in neurofibromatosis type 1
• Mosaicism in HIF2A-related polycythemia-paraganglioma syndrome
• Multiple Endocrine Neoplasia: Spectrum of Abdominal Manifestations
• Neoplasms of the Neuroendocrine Pancreas: An Update in the Classification, Definition, and Molecular Genetic Advances
• Neuraxial dysraphism in <em>EPAS1-</em>associated syndrome due to improper mesenchymal transition
• Neuroendocrine neoplasia and bone (Review)
• Neuroendocrine tumour in a patient with neurofibromatosis type 1 and HIV
• Neurofibromatosis type 1, gastrointestinal stromal tumor, leiomyosarcoma and osteosarcoma: four cases of rare tumors and a review of the literature
• New considerations in the surgical treatment of pancreatic neuroendocrine tumours
• New syndrome of paraganglioma and somatostatinoma associated with polycythemia
• Nonmosaic somatic HIF2A mutations associated with late onset polycythemia-paraganglioma syndrome: Newly recognized subclass of polycythemia-paraganglioma syndrome
• Novel HIF2A mutations disrupt oxygen sensing, leading to polycythemia, paragangliomas, and somatostatinomas
• Novel insights into the polycythemia-paraganglioma-somatostatinoma syndrome
• Ocular manifestations of hypoxia-inducible factor-2alpha paraganglioma-somatostatinoma-polycythemia syndrome
• Ocular manifestations of hypoxia-inducible factor-2α paraganglioma-somatostatinoma-polycythemia syndrome
• Pacak-Zhuang syndrome: a model providing new insights into tumor syndromes
• Pancreatic neuroendocrine neoplasms: Clinicopathological features and pathological staging
• Pancreatic neuroendocrine tumors: clinical features, diagnosis and medical treatment: advances
• Pancreatic neuroendocrine tumors: contemporary diagnosis and management
• Pancreatic somatostatinoma diagnosed preoperatively: report of a case
• Patient with adult-onset type II citrullinemia beginning 2 years after operation for duodenal malignant somatostatinoma: Indication for liver transplantation
• PGP 9.5 immunocytochemical staining for pancreatic endocrine tumors
• Polycythemia and paraganglioma with a novel somatic HIF2A mutation in a male
• Prognostic relevance of proliferation-related miRNAs in pancreatic neuroendocrine neoplasms
• Somatic mosaicism of EPAS1 mutations in the syndrome of paraganglioma and somatostatinoma associated with polycythemia
• Somatostatin-derived amyloidosis: a novel type of amyloidosis associated with well-differentiated somatostatin-producing neuroendocrine tumours
• Somatostatin-Immunoreactive Pancreaticoduodenal Neuroendocrine Neoplasms: Twenty-Three Cases Evaluated according to the WHO 2010 Classification
• Somatostatin-producing duodenal carcinoma: clinicopathological description of a case
• Somatostatinoma
• Somatostatinoma
• Somatostatinoma and Neurofibromatosis Type 1-A Case Report and Review of the Literature
• Somatostatinoma Masquerading as Chronic Pancreatitis
• Somatostatinoma of the Ampulla of Vater: A Systematic Review
• Somatostatinoma of the Ampulla: An Incidental Postoperative Finding Following Colorectal Cancer Resection
• Somatostatinoma of the minor duodenal papilla associated with pancreas divisum treated by endoscopic papillectomy
• Somatostatinoma of the minor papilla treated by local excision in a patient with neurofibromatosis type 1
• Somatostatinoma Presented as Double-Duct Sign
• Somatostatinoma syndrome: a challenging differential diagnosis among pancreatic tumors
• Somatostatinoma: Beyond neurofibromatosis type 1 (Review)
• The Coexistence of Somatostatinoma and Gastrointestinal Stromal Tumor in the Duodenum of a Patient with Von Recklinghausen's Disease
• Vascular Changes in the Retina and Choroid of Patients With EPAS1 Gain-of-Function Mutation Syndrome