Disease: Pyogenic arthritis- pyoderma gangrenosum- and acne
- A case of autoinflammatory skin and bone disease flared by a change in osteoporosis management
- A case of myeloperoxidase-antineutrophil cytoplasmic antibody and anticardiolipin antibody-positive pyogenic arthritis, pyoderma gangrenosum, acne and hidradenitis suppurativa (PAPASH) syndrome with colitis
- A child with recurrent pyogenic arthritis with the PSTPIP1 mutation
- A clinical update on inflammasomopathies
- A dermatologic perspective on autoinflammatory diseases
- A pregnancy-associated nonfamilial case of PAPA (pyogenic sterile arthritis, pyoderma gangrenosum, acne) syndrome
- A Unified Concept of Acne in the PAPA Spectrum Disorders
- Acne Conglobata
- Acne Conglobata
- Alarming consequences - autoinflammatory disease spectrum due to mutations in proline-serine-threonine phosphatase-interacting protein 1
- Altered keratinization and vitamin D metabolism may be key pathogenetic pathways in syndromic hidradenitis suppurativa: a novel whole exome sequencing approach
- Anakinra in Pyogenic Arthritis, Acne, Pyoderma Gangrenosum, and Suppurative Hidradenitis (PAPASH) Spectrum Disorder: A Case Report and Literature Review
- Ancient friends, revisited: Systematic review and case report of pyoderma gangrenosum-associated autoinflammatory syndromes
- Are neutrophilic dermatoses autoinflammatory disorders?
- Autoinflammatory diseases in childhood, part 1: monogenic syndromes
- Autoinflammatory syndromes associated with hidradenitis suppurativa and/or acne
- Case Report: PsAPSASH syndrome: an alternative phenotype of syndromic hidradenitis suppurativa treated with the IL-17A inhibitor secukinumab
- Case Report: Pyogenic Arthritis, Pyoderma Gangrenosum, and Acne: A Single-Center Experience and Literature Review
- Cerebral vascular findings in PAPA syndrome: cerebral arterial vasculopathy or vasculitis and a posterior cerebral artery dissecting aneurysm
- Cerebral vascular findings in PAPA syndrome: cerebral arterial vasculopathy or vasculitis and a posterior cerebral artery dissecting aneurysm
- Clinical analysis of 49 cases of non-inflammasome related conditions
- Clinical and genetic analysis of the first Mexican patient with a diagnosis of pyogenic sterile arthritis, pyoderma gangrenosum and acne (PAPA) syndrome
- Clinical and genetic characteristics of PSTPIP1-associated myeloid-related proteinemia inflammatory syndrome
- Clinical and Genetic Findings of the First Report of PAPA Syndrome in Brazil
- Detection of a rare variant in PSTPIP1 through three generations in a family with an initial diagnosis of FMF/MKD-overlapping phenotype
- Diagnosis and Clinical Examination of Autoinflammatory Syndrome
- Difficult and rare forms of acne
- Disease activity accounts for long-term efficacy of IL-1 blockers in pyogenic sterile arthritis pyoderma gangrenosum and severe acne syndrome
- Dysregulated neutrophil responses and neutrophil extracellular trap formation and degradation in PAPA syndrome
- Efficacy and safety of anakinra and canakinumab in PSTPIP1-associated inflammatory diseases: a comprehensive scoping review
- Excess Serum Interleukin-18 Distinguishes Patients With Pathogenic Mutations in PSTPIP1
- Familial Mediterranean fever patients with hidradenitis suppurativa
- First nicastrin mutation in PASH (pyoderma gangrenosum, acne and suppurative hidradenitis) syndrome
- Genetic mutations in pyoderma gangrenosum, hidradenitis suppurativa, and associated autoinflammatory syndromes: Insights into pathogenic mechanisms and shared pathways
- Haematological involvement associated with a mild autoinflammatory phenotype, in two patients carrying the E250K mutation of PSTPIP1
- Hidradenitis suppurativa and Mediterranean fever gene mutations
- Hidradenitis Suppurativa in a Patient with Smith-Magenis Syndrome: A Case Report
- Hidradenitis Suppurativa-Related Autoinflammatory Syndromes: An Updated Review on the Clinics, Genetics, and Treatment of Pyoderma gangrenosum, Acne and Suppurative Hidradenitis (PASH), Pyogenic Arthritis, Pyoderma gangrenosum, Acne and Suppurative Hidrad
- High level of serum human interleukin-18 in a patient with pyogenic arthritis, pyoderma gangrenosum and acne syndrome
- Identification of novel mutations in CD2BP1 gene in clinically proven rheumatoid arthritis patients of south India
- Imaging findings of sterile pyogenic arthritis, pyoderma gangrenosum and acne (PAPA) syndrome: differential diagnosis and review of the literature
- Interrupting an IFN-gamma-dependent feedback loop in the syndrome of pyogenic arthritis with pyoderma gangrenosum and acne
- Interrupting an IFN-γ-dependent feedback loop in the syndrome of pyogenic arthritis with pyoderma gangrenosum and acne
- Kidney Involvement in PSTPIP1 Associated Inflammatory Diseases (PAID): A Case Report and Review of the Literature
- Monogenic Auto-inflammatory Syndromes: A Review of the Literature
- Multilocular pyoderma gangrenosum : Association with primary manifestation of primary biliary cholangitis
- Mutation in the proline-serine-threonine phosphatase-interacting protein 1 (<em>PSTPIP1</em>) gene in a patient with acute lymphoblastic leukemia
- Neutrophilic dermatoses: Kids are not just little people
- New described dermatological disorders
- Next-Generation Sequencing Analysis of MVK, NLRP3, TNFRSF1A, and PSTPIP1 Genes in Patients without MEFV Gene Variation and Genotype-Phenotype Correlation
- Novel PSTPIP1 gene mutation in a patient with pyogenic arthritis, pyoderma gangrenosum and acne (PAPA) syndrome
- Osteolytic lesion in PAPA syndrome responding to anti-interleukin 1 treatment
- Overall and subgroup prevalence of pyoderma gangrenosum among patients with hidradenitis suppurativa: A population-based analysis in the United States
- PAPA and FMF in two siblings: possible amplification of clinical presentation? A case report
- PAPA spectrum disorders
- PAPA syndrome with Crohn's disease and primary sclerosing cholangitis/autoimmune hepatitis overlap syndrome
- PAPA Syndrome: Challenges in Achieving Long-Term Remission
- PAPA-like syndrome with heterozygous mutation in the MEFV gene
- PAPA, PASH and PAPASH Syndromes: Pathophysiology, Presentation and Treatment
- PAPASH, PsAPASH and PASS autoinflammatory syndromes: phenotypic heterogeneity, common biological signature and response to immunosuppressive regimens
- Pathogenesis and Clinical Examination of Autoinflammatory Syndrome
- Pathogenic roles and diagnostic utility of interleukin-18 in autoinflammatory diseases
- Pattern and diagnostic evaluation of systemic autoinflammatory diseases other than familial Mediterranean fever among Arab children: a multicenter study from the Pediatric Rheumatology Arab Group (PRAG)
- Pediatric Pyoderma Gangrenosum: A Retrospective Review of Clinical Features, Etiologic Associations, and Treatment
- Pediatric pyoderma gangrenosum: a systematic review and update
- Phenotypes and Pathophysiology of Syndromic Hidradenitis Suppurativa: Different Faces of the Same Disease? A Systematic Review
- Phenotypic Associations of PSTPIP1 Sequence Variants in PSTPIP1-Associated Autoinflammatory Diseases
- PsAPASH: a new syndrome associated with hidradenitis suppurativa with response to tumor necrosis factor inhibition
- PsAPASH: a rare and recent autoinflammatory syndrome associated with hidradenitis suppurativa
- PSTPIP1-associated myeloid-related proteinaemia inflammatory (PAMI) syndrome; a case presenting as a perinatal event with early central nervous system involvement?
- Pyoderma gangrenosum and its syndromic forms: evidence for a link with autoinflammation
- Pyoderma gangrenosum and suppurative hidradenitis association, overlap or spectrum of the same disease? Case report and discussion
- Pyoderma gangrenosum, acne and ulcerative colitis in a patient with a novel mutation in the PSTPIP1 gene
- Pyoderma gangrenosum, acne, and hidradenitis suppurativa (PASH) syndrome with recurrent vasculitis
- Pyoderma Gangrenosum, Acne, and Hidradenitis Suppurativa Syndrome: A Case Report and Literature Review
- Pyogenic arthritis pyoderma gangrenosum and acne syndrome: A rare but important diagnosis for antibiotic-resistant erysipelas-like erythema and osteonecrosis
- Pyogenic Arthritis, Pyoderma Gangrenosum, Acne, Suppurative Hidradenitis (PA-PASH) Syndrome: An Atypical Presentation of a Rare Syndrome
- Pyogenic arthritis, pyoderma gangrenosum, and acne (PAPA) syndrome: differential diagnosis of septic arthritis by regular detection of exceedingly high synovial cell counts
- Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome in a Chinese family: A case report and review of literature
- Rare Case of Pyoderma Gangrenosum in the Setting of PAPA Syndrome in a 12-Year-Old Child
- Rare missense variants in the SH3 domain of <em>PSTPIP1</em> are associated with hidradenitis suppurativa
- Recent Insights in Pyrin Inflammasome Activation: Identifying Potential Novel Therapeutic Approaches in Pyrin-Associated Autoinflammatory Syndromes
- Renal involvement as a potential feature of pyogenic arthritis, pyoderma gangrenosum, and acne syndrome with E250K mutation of PSTPIP1 gene
- Severe acne in autoinflammatory diseases
- Single amino acid charge switch defines clinically distinct proline-serine-threonine phosphatase-interacting protein 1 (PSTPIP1)-associated inflammatory diseases
- State of care for patients with systemic autoinflammatory diseases - Results of a tertiary care survey
- Successful combined antibiotic therapy with oral clindamycin and oral rifampicin for pyoderma gangrenosum in patient with PASH syndrome
- Successful Treatment of PAPA Syndrome with Dual Adalimumab and Tacrolimus Therapy
- Successful treatment of PAPA syndrome with minocycline, dapsone, deflazacort and methotrexate: a cost-effective therapy with a 2-year follow-up
- Sweet Syndrome
- Sweet Syndrome
- Systematic evaluation of nine monogenic autoinflammatory diseases reveals common and disease-specific correlations with allergy-associated features
- Targeted therapy of pyogenic sterile arthritis, pyoderma gangrenosum, and acne syndrome (PAPA): a case report and literature review
- The expanding spectrum of clinical phenotypes associated with PSTPIP1 mutations: from PAPA to PAMI syndrome and beyond
- The genetics of pyoderma gangrenosum and implications for treatment: a systematic review
- The Relationship between NALP3 and Autoinflammatory Syndromes
- The role of interleukin-1beta in pyoderma gangrenosum
- The role of interleukin-1β in pyoderma gangrenosum
- Vasculitis in Systemic Autoinflammatory Diseases
- Web Exclusive. Annals Story Slam - Papa Is on a Ventilator