Disease: Glycogenosis type 8
- 104-week efficacy and safety of cipaglucosidase alfa plus miglustat in adults with late-onset Pompe disease: a phase III open-label extension study (ATB200-07)
- A 78-year-old Japanese male with late-onset PHKA1-associated distal myopathy: Case report and literature review
- A Broad Characterization of Glycogen Storage Disease IV Patients: A Clinical, Genetic, and Histopathological Study
- A case report of Danon's disease with dilated phenotype
- A novel likely pathogenic homozygous RBCK1 variant in dilated cardiomyopathy with muscle weakness
- A rare and fatal cause of hypertrophic cardiomyopathy: Danon disease
- AAV-mediated delivery of secreted acid α-glucosidase with enhanced uptake corrects neuromuscular pathology in Pompe mice
- Accuracy and impact on quality of life of real-time continuous glucose monitoring in children with hyperinsulinaemic hypoglycaemia
- Acute ketone supplementation in the absence of muscle glycogen utilization: Insights from McArdle disease
- An analysis of Pompe newborn screening data: a new prevalence at birth, insight and discussion
- An Unusual Case of Neonatal Hypotonia and Femur Fracture: Neuromuscular Variant of Glycogen Storage Disease Type IV
- An updated management approach of Pompe disease patients with high-sustained anti-rhGAA IgG antibody titers: experience with bortezomib-based immunomodulation
- Analysis of lysosomal enzyme activity and genetic variants in a child with late-onset Pompe disease
- Assessment of auditory functions in patients with hepatic glycogen storage diseases
- Assessment of the function and morphology of the thyroid gland in paediatric patients treated with enzyme replacement therapy due to selected storage diseases - preliminary results of our own research and a review of the literature
- Atraumatic Acute Paraspinal Compartment Syndrome in a Patient With McArdle's Disease
- Bedtime extended release cornstarch improves biochemical profile and sleep quality for patients with glycogen storage disease type Ia
- Blood glucose trends in glycogen storage disease type Ia: A cross-sectional study
- BNIP3 Is Involved in Muscle Fiber Atrophy in Late-Onset Pompe Disease Patients
- Body composition in patients with hepatic glycogen storage diseases
- Changes in forced vital capacity over 13 years among patients with late-onset Pompe disease treated with alglucosidase alfa: new modeling of real-world data from the Pompe Registry
- Cipaglucosidase Alfa: First Approval
- Clinical characteristics and long-term outcomes of patients with glycogen storage disease type 1b: a retrospective multi-center experience in Poland
- Clinical features of pediatric Danon disease and the importance of early diagnosis
- Clinical manifestations and acid alpha-glucosidase mutation characterisation of a cohort of patients with late-onset Pompe disease in eastern China
- Cytokine profiling in patients with hepatic glycogen storage disease: Are there clues for unsolved aspects?
- Danon Disease: Entire <em>LAMP2</em> Gene Deletion with Unusual Clinical Presentation-Case Report and Review of the Literature
- Danon Disease: Entire LAMP2 Gene Deletion with Unusual Clinical Presentation-Case Report and Review of the Literature
- Dapagliflozin and Empagliflozin in Paediatric Indications: A Systematic Review
- Defect in degradation of glycogenin-exposed residual glycogen in lysosomes is the fundamental pathomechanism of Pompe disease
- Degeneration of muscle spindles in a murine model of Pompe disease
- Domino liver transplantation for maple syrup urine disease in children: A single-center case series
- Dose-response effect of pre-exercise carbohydrates under muscle glycogen unavailability: Insights from McArdle disease
- Early clinical phenotype of late onset Pompe disease: Lessons learned from newborn screening
- Effectiveness and safety of the treatment of lysosomal deposit diseases: Analysis of 22 patients
- Effects of enzyme replacement therapy on cardiac function in classic infantile Pompe disease
- Efficacious Androgen Hormone Administration in Combination with Adeno-Associated Virus Vector-Mediated Gene Therapy in Female Mice with Pompe Disease
- Efficacy and Safety of Avalglucosidase Alfa in Patients With Late-Onset Pompe Disease After 97 Weeks: A Phase 3 Randomized Clinical Trial
- Efficacy and safety of empagliflozin in glycogen storage disease type Ib: Data from an international questionnaire
- Elucidation of intermolecular interactions between chlorogenic acid and glucose-6-phosphate translocase: A step towards chemically induced glycogen storage disease type 1b model
- Empagliflozin for treating neutropenia and neutrophil dysfunction in 21 infants with glycogen storage disease 1b
- Enzyme replacement therapy and immunotherapy lead to significant functional improvement in two children with Pompe disease: a case report
- Enzyme replacement therapy for late-onset Pompe disease
- Evaluating brain white matter hyperintensity, IQ scores, and plasma neurofilament light chain concentration in early-treated patients with infantile-onset Pompe disease
- Exosomal MicroRNAs as Potential Biomarkers of Hepatic Injury and Kidney Disease in Glycogen Storage Disease Type Ia Patients
- Favorable outcome of empagliflozin treatment in two pediatric glycogen storage disease type 1b patients
- Features of chinese patients with sitosterolemia
- Harnessing polyhydroxylated pyrrolidines as a stabilizer of acid alpha-glucosidase (GAA) to enhance the efficacy of enzyme replacement therapy in Pompe disease
- High childhood serum triglyceride concentrations associate with hepatocellular adenoma development in patients with glycogen storage disease type Ia
- High prevalence of paraspinal muscle involvement in adults with McArdle disease
- Home-Based Infusion of Alglucosidase Alfa Can Safely be Implemented in Adults with Late-Onset Pompe Disease: Lessons Learned from 18,380 Infusions
- Implementation of Newborn Screening for Conditions in the United States First Recommended during 2010-2018
- Intracranial vasculopathy: an important organ damage in young adult patients with late-onset Pompe disease
- Investigation on the treatment of empagliflozin in glycogen storage disease type b
- Investigation on the treatment of empagliflozin in glycogen storage disease type Ib
- Involvement of muscle satellite cell dysfunction in neuromuscular disorders: Expanding the portfolio of satellite cell-opathies
- L-alanine supplementation in Pompe disease (IOPD): a potential therapeutic implementation for patients on ERT? A case report
- Late onset Pompe disease: an analysis of 19 patients from Mexico
- Long term survival in patients with classic infantile Pompe disease reveals a spectrum with progressive brain abnormalities and changes in cognitive functioning
- Long-Term Exercise Intervention in Patients with McArdle Disease: Clinical and Aerobic Fitness Benefits
- Long-Term Experience with Anaphylaxis and Desensitization to Alglucosidase Alfa in Pompe Disease
- Long-term safety and efficacy of cipaglucosidase alfa plus miglustat in individuals living with Pompe disease: an open-label phase I/II study (ATB200-02)
- Long-Term Treatment of Lipoprotein Lipase Deficiency with Medium-Chain Triglyceride-Enriched Diet: A Case Series
- McArdle disease in a patient with anorexia nervosa: a case report
- Mild disease course of SARS-CoV-2 infections and mild side effects of vaccination in Pompe disease: a cohort description
- Minimal clinically important differences in six-minute walking distance in late-onset Pompe disease
- Minimum Effective Dose to Achieve Biochemical Correction with Adeno-Associated Virus Vector-Mediated Gene Therapy in Mice with Pompe Disease
- Motor Responses in Pediatric Pompe Disease in the ADVANCE Participant Cohort
- Muscle diffusion MRI reveals autophagic buildup in a mouse model for Pompe disease
- Muscle MRI in McArdle Disease: A European Multicenter Observational Study
- Mutational analysis and clinical investigations of medically diagnosed GSD 1a patients from Pakistan
- Neurofilament Light and Its Association With CNS Involvement in Patients With Classic Infantile Pompe Disease
- Neutrophil functions in patients with neutropenia due to glycogen storage disease type 1b treated with empagliflozin
- Novel Mutation in the Feline <em>GAA</em> Gene in a Cat with Glycogen Storage Disease Type II (Pompe Disease)
- Novel Mutation in the Feline GAA Gene in a Cat with Glycogen Storage Disease Type II (Pompe Disease)
- Paediatric hepatocellular adenomas: Lessons from a systematic review of relevant literature
- Patient-reported outcomes on empagliflozin treatment in glycogen storage disease type Ib: An international questionnaire study
- Phase I study of liver depot gene therapy in late-onset Pompe disease
- Physical training and high-protein diet improved muscle strength, parent-reported fatigue, and physical quality of life in children with Pompe disease
- Pompe disease misdiagnosed as polymyositis
- Potential use of other starch sources in the treatment of glycogen storage disease type Ia - an in vitro study
- Rapid ultra-performance liquid chromatography-tandem mass spectrometry method for the simultaneous determination of three characteristic urinary saccharide metabolites in patients with glycogen storage diseases (type b and )
- Rapid ultra-performance liquid chromatography-tandem mass spectrometry method for the simultaneous determination of three characteristic urinary saccharide metabolites in patients with glycogen storage diseases (type Ⅰb and Ⅱ)
- Rare disease therapeutics: The future of medical genetics in a changing landscape
- Real-world outcomes from a series of patients with late onset Pompe disease who switched from alglucosidase alfa to avalglucosidase alfa
- Real-world patient data on immunity and COVID-19 status of patients with MPS, Gaucher, and Pompe diseases from Turkey
- Right Ventricle Involvement by Glycogen Storage Cardiomyopathy (PRKAG2): Standard and Advanced Echocardiography Analyses
- Safety and effectiveness of resistance training in patients with late onset Pompe disease - a pilot study
- Safety outcomes and patients' preferences for home-based intravenous enzyme replacement therapy (ERT) in pompe disease and mucopolysaccharidosis type I (MPS I) disorder: COVID-19 and beyond
- Severe neuromuscular forms of glycogen storage disease type IV: Histological, clinical, biochemical, and molecular findings in a large French case series
- SLGT2 Inhibitor Rescues Myelopoiesis in G6PC3 Deficiency
- Successful AAV8 readministration: Suppression of capsid-specific neutralizing antibodies by a combination treatment of bortezomib and CD20 mAb in a mouse model of Pompe disease
- Two fluorimetric determinations of acid alpha-glucosidase activity in dried blood spot: Pompe disease in Iranian population
- Two fluorimetric determinations of acid α-glucosidase activity in dried blood spot: Pompe disease in Iranian population
- Two fluorimetric determinations of acid α-glucosidase activity in dried-blood spot: Pompe disease in Iranian population
- Understanding the role of SGLT2 inhibitors in glycogen storage disease type Ib: the experience of one UK centre
- Validation of the Patient-Reported Outcomes Measurement Information System (PROMIS()) physical function questionnaire in late-onset Pompe disease using PROPEL phase 3 data
- Validation of the Patient-Reported Outcomes Measurement Information System (PROMIS<sup>®</sup>) physical function questionnaire in late-onset Pompe disease using PROPEL phase 3 data
- Whole-exome sequencing detects <em>PYGM</em> variants in two adults with McArdle disease
- Whole-exome sequencing detects PYGM variants in two adults with McArdle disease