Disease: Dysmyelination
- <em>PLEKHG5</em>-related autosomal recessive lower motor neuron disease with dysmyelination in peripheral nerves
- A class-specific effect of dysmyelination on the excitability of hippocampal interneurons
- A hypomyelinating leukodystrophy in German Shepherd dogs
- A Mouse Model System to Study Peroxisomal Roles in Neurodegeneration of Peroxisome Biogenesis Disorders
- A novel case of concurrent occurrence of demyelinating-polyneuropathy-causing PMP22 duplication and SOX10 gene mutation producing severe hypertrophic neuropathy
- A novel mouse model of CMT1B identifies hyperglycosylation as a new pathogenetic mechanism
- A Novel Vitronectin Peptide Facilitates Differentiation of Oligodendrocytes from Human Pluripotent Stem Cells (Synthetic ECM for Oligodendrocyte Differentiation)
- A role of oligodendrocytes in information processing
- Abnormalities of Cerebral White Matter Microstructure in Children With New-Onset, Untreated Idiopathic-Generalized Epilepsy
- Age-Dependent Increase in Schmidt-Lanterman Incisures and a Cadm4-Associated Membrane Skeletal Complex in Fatty Acid 2-hydroxylase Deficient Mice: a Mouse Model of Spastic Paraplegia SPG35
- Alpha-Asaronol Alleviates Dysmyelination by Enhancing Glutamate Transport Through the Activation of PPARgamma-GLT-1 Signaling in Hypoxia-Ischemia Neonatal Rats
- Alpha-Asaronol Alleviates Dysmyelination by Enhancing Glutamate Transport Through the Activation of PPARγ-GLT-1 Signaling in Hypoxia-Ischemia Neonatal Rats
- Alpha-asaronol promoted oligodendrocyte precursor cell differentiation and improved myelination as an activator PPARγ
- Alterations of Oligodendrocyte and Myelin Energy Metabolism in Multiple Sclerosis
- Alzheimer's disease alters oligodendrocytic glycolytic and ketolytic gene expression
- Assembly and Function of the Juxtaparanodal Kv1 Complex in Health and Disease
- Assessing regional intracortical myelination in schizophrenia spectrum and bipolar disorders using the optimized T1w/T2w-ratio
- Assessment of myelination in infants and young children by T1 relaxation time measurements using the magnetization-prepared 2 rapid acquisition gradient echoes sequence
- Association between Diffusion Tensor Imaging, inflammation and immunological alterations in unipolar and bipolar depression: A review
- Associations of alcohol use, HIV infection, and age with brain white matter microstructure
- Baroreflex sensitivity is associated with markers of hippocampal gliosis and dysmyelination in patients with psychosis
- Canine models of Charcot-Marie-Tooth: MTMR2, MPZ, and SH3TC2 variants in golden retrievers with congenital hypomyelinating polyneuropathy
- Case of acute onset ataxia caused by <em>Klebsiella pneumoniae</em> sepsis with the appearance of anti-GD1b antibody
- CIDP, CMT1B, or CMT1B plus CIDP?
- Clinical and genetic spectrum of hereditary spastic paraplegia in Chinese children
- Cognitive Dysfunction After Analgesia and Sedation: Out of the Operating Room and Into the Pediatric Intensive Care Unit
- Comparative role of SOX10 gene in the gliogenesis of central, peripheral, and enteric nervous systems
- Conduction slowing, conduction block and temporal dispersion in demyelinating, dysmyelinating and axonal neuropathies: Electrophysiology meets pathology
- COVID-19 Proned Ventilation and Its Possible Association With Foot Drop: A Case Series
- Curcumin-cyclodextrin/cellulose nanocrystals improve the phenotype of Charcot-Marie-Tooth-1A transgenic rats through the reduction of oxidative stress
- Deficiency of galactosy-lceramidase in adult oligodendrocytes worsens disease severity during chronic experimental allergic encephalomyelitis
- Deficiency of galactosyl-ceramidase in adult oligodendrocytes worsens disease severity during chronic experimental allergic encephalomyelitis
- Deficiency of galactosylceramidase in adult oligodendrocytes worsens the neurological deficits and shortens the survival during chronic experimental allergic encephalomyelitis
- Deletion of the Thrombin Proteolytic Site in Neurofascin 155 Causes Disruption of Nodal and Paranodal Organization
- Distinct Changes in Calpain and Calpastatin during PNS Myelination and Demyelination in Rodent Models
- Docking protein 6 (DOK6) selectively docks the neurotrophic signaling transduction to restrain peripheral neuropathy
- Downregulation of PMP22 ameliorates myelin defects in iPSC-derived human organoid cultures of CMT1A
- Dysmyelination and glycolipid interference caused by phenylalanine in phenylketonuria
- Dysmyelination by Oligodendrocyte-Specific Ablation of Ninj2 Contributes to Depressive-Like Behaviors
- Early Changes in Skeletal Muscle of Young C22 Mice, A Model of Charcot-Marie-Tooth 1A
- Epidural Anesthesia and Continuous Epidural Analgesia in a Pediatric Patient With Pelizaeus-Merzbacher Disease: A Case Report
- Ermin deficiency leads to compromised myelin, inflammatory milieu, and susceptibility to demyelinating insult
- Exosomal Lipid Biomarkers of Oligodendrocyte Pathology to Predict Scoliosis in Children with Cerebral Palsy
- Fibulin 5, a human Wharton's jelly-derived mesenchymal stem cells-secreted paracrine factor, attenuates peripheral nervous system myelination defects through the Integrin-RAC1 signaling axis
- Four mutations in MITF, SOX10 and PAX3 genes were identified as genetic causes of waardenburg syndrome in four unrelated Iranian patients: case report
- Further delineation of HIDEA syndrome
- Glial progenitor cell-based repair of the dysmyelinated brain: Progression to the clinic
- Gut and oral microbiome modulate molecular and clinical markers of schizophrenia-related symptoms: A transdiagnostic, multilevel pilot study
- HDAC3 Inhibition Stimulates Myelination in a CMT1A Mouse Model
- Histopathology of the trigeminal ganglion and nerve: A historical review
- Human stem cell-derived oligodendrocytes: From humanized animal models to cell therapy in myelin diseases
- Hypomyelinating leukodystrophies in adults: Clinical and genetic features
- Impaired Autophagy in Krabbe Disease: The Role of BCL2 and Beclin-1 Phosphorylation
- In Silico Structural Analysis Predicting the Pathogenicity of PLP1 Mutations in Multiple Sclerosis
- Inhomogeneous magnetization transfer MRI of white matter structures in the hypomyelinated shiverer mouse brain
- Interference of commissural connections through the genu of the corpus callosum specifically impairs sensorimotor gating
- Intermittent lipid nanoparticle mRNA administration prevents cortical dysmyelination associated with arginase deficiency
- Intracarotid Transplantation of Skin-Derived Precursor Schwann Cells Promotes Functional Recovery After Acute Ischemic Stroke in Rats
- Jitter patterns in conventional concentric needle electromyography recordings of regenerating motor units
- Loss of oligodendrocyte ErbB receptor signaling leads to hypomyelination, reduced density of parvalbumin-expressing interneurons, and inhibitory function in the auditory cortex
- Magnetic Resonance Imaging and Spectroscopy Analysis in a Pelizaeus-Merzbacher Disease Rat Model
- Magnetic resonance imaging of disorders with white matter changes in children and adolescents: a pictorial essay
- Maternal Blood Lipid Biomarkers of Oligodendrocyte Pathology to Predict Fetal Alcohol Spectrum Disorders
- Mechanisms and treatment strategies of demyelinating and dysmyelinating Charcot-Marie-Tooth disease
- Mek/ERK1/2-MAPK and PI3K/Akt/mTOR signaling plays both independent and cooperative roles in Schwann cell differentiation, myelination and dysmyelination
- Melatonin pretreatment alleviates the long-term synaptic toxicity and dysmyelination induced by neonatal Sevoflurane exposure via MT1 receptor-mediated Wnt signaling modulation
- Metformin treatment reduces inflammation, dysmyelination and disease severity in a mouse model of multiple sclerosis, experimental autoimmune encephalomyelitis
- Microglia-Mediated Neurodegeneration in Perinatal Brain Injuries
- Movement disorders in hereditary spastic paraplegias
- Myelin Defects in Niemann-Pick Type C Disease: Mechanisms and Possible Therapeutic Perspectives
- Myelin in Alzheimer's disease: culprit or bystander?
- Myelin-Independent Therapeutic Potential of Canine Glial-Restricted Progenitors Transplanted in Mouse Model of Dysmyelinating Disease
- Myelination synchronizes cortical oscillations by consolidating parvalbumin-mediated phasic inhibition
- Nanoscale volumetric fluorescence imaging via photochemical sectioning
- Nanostructure-specific X-ray tomography reveals myelin levels, integrity and axon orientations in mouse and human nervous tissue
- Neurological Manifestations of Congenital Cytomegalovirus Infection at a Tertiary Care Centre from Southern India
- Neurological Waardenburg-Shah syndrome: a diagnostic challenge in a child with skin hypopigmentation and neurological manifestation
- Novel <em>SOX10</em> Mutations in Waardenburg Syndrome: Functional Characterization and Genotype-Phenotype Analysis
- Novel Homozygous FA2H Variant Causing the Full Spectrum of Fatty Acid Hydroxylase-Associated Neurodegeneration (SPG35)
- Novel syndromic neurodevelopmental disorder caused by <em>de novo</em> deletion of <em>CHASERR</em>, a long noncoding RNA
- Novel syndromic neurodevelopmental disorder caused by de novo deletion of <em>CHASERR</em> , a long noncoding RNA
- Oligodendrocyte pathology in fetal alcohol spectrum disorders
- Oligodendrocyte pathology in Huntington's disease: from mechanisms to therapeutics
- Oligodendrocyte Precursor Cells Transplantation Improves Stroke Recovery <em>via</em> Oligodendrogenesis, Neurite Growth and Synaptogenesis
- Pelizaeus-Merzbacher Disease with <em>PLP1</em> Exon 1 Duplication, Previously Misdiagnosed as Cerebral Palsy: a Case Report
- PLEKHG5-related autosomal recessive lower motor neuron disease with dysmyelination in peripheral nerves
- Promyelinating drugs promote functional recovery in an autism spectrum disorder mouse model of Pitt-Hopkins syndrome
- Rac1 and Rac3 have opposite functions in Schwann cells during developmental myelination
- Renewal of oligodendrocyte lineage reverses dysmyelination and CNS neurodegeneration through corrected N-acetylaspartate metabolism
- Role of SNAREs and Rabs in Myelin Regulation
- SARM1 knockout does not rescue neuromuscular phenotypes in a Charcot-Marie-Tooth disease Type 1A mouse model
- Secondary Degeneration Impairs Myelin Ultrastructural Development in Adulthood following Adolescent Neurotrauma in the Rat Optic Nerve
- Severe DNM1 encephalopathy with dysmyelination due to recurrent splice site pathogenic variant
- Soluble dimeric prion protein ligand activates Adgrg6 receptor but does not rescue early signs of demyelination in PrP-deficient mice
- SOX10: 20 years of phenotypic plurality and current understanding of its developmental function
- Sulfatide in health and disease. The evaluation of sulfatide in cerebrospinal fluid as a possible biomarker for neurodegeneration
- Temporal pole blurring in temporal lobe epilepsy revealed by 3D Edge-Enhancing Gradient Echo MRI
- The pathogenesis of, and pharmacological treatment for, Canavan disease
- Transplantation of Human Glial Progenitors to Immunodeficient Neonatal Mice with Amyotrophic Lateral Sclerosis (SOD1/rag2)
- Utilizing hiPSC-derived oligodendrocytes to study myelin pathophysiology in neuropsychiatric and neurodegenerative disorders