• A Case Report of Central Bronchiectasis in a Poorly Controlled Asthmatic Adolescent With Allergic Bronchopulmonary Aspergillosis and Secondary Spontaneous Pneumothorax
• A randomised crossover trial of tezacaftor-ivacaftor for gut dysfunction in cystic fibrosis with magnetic resonance imaging (MRI) outcomes: a pilot study
• ABC transporters involved in respiratory and cholestatic diseases: From rare to very rare monogenic diseases
• Accurate and Automated Genotyping of the <em>CFTR</em> Poly-T/TG Tract with <em>CFTR</em>-TIPS
• Adverse effects of the tezacaftor/ivacaftor/elexacaftor combination that may lead to discontinuation: About a series of 10 cases
• Allergic bronchopulmonary aspergillosis as an initial manifestation of cystic fibrosis: Diagnostic and therapeutic implications in the era of CFTR modulators
• Allosteric inhibition of CFTR gating by CFTRinh-172 binding in the pore
• Antibacterial and antibiofilm effect of Zinc Oxide nanoparticles on P. aeruginosa variants isolated from young patients with cystic fibrosis
• Antibody-Mediated Rejection in Lung Transplantation: Diagnosis and Therapeutic Armamentarium in a 21st Century Perspective
• Artificial intelligence-driven volumetric CT outcome score in cystic fibrosis: longitudinal and multicenter validation with/without modulators treatment
• Assessing alternative treatment targets in patients with cystic fibrosis
• Associations between chronic rhinosinusitis and the development of non-cystic fibrosis bronchiectasis
• Asthma severity: the patient's point of view
• Blood Transcriptomic and Inflammatory Protein Biomarkers Associated with Imminent Pulmonary Exacerbation Risk in Cystic Fibrosis
• Breaking new ground in COPD imaging: 3D-PREFUL MRI versus traditional techniques
• Burden of rare genetic disorders in India: twenty-two years' experience of a tertiary centre
• Burkholderia cenocepacia ST-250 in cystic fibrosis patients in Switzerland: Genomic investigation of transmission routes
• Burkholderia cepacia Complex Producing a Peculiar Violet Pigment: A Case Series From a Tertiary Care Hospital in Meghalaya
• Ceftolozane/Tazobactam for the Treatment of Adults With Cystic Fibrosis: Results From a French Prospective Cohort Study
• CFTR and colorectal cancer susceptibility: an urgent need for further studies
• CFTR Modulators Therapy Efficacy in Reducing Cystic Fibrosis (CF) Exacerbation and Improving Selected Spirometry Parameters: A Real-Life Study in a Single-Centre Polish Population
• Clinical perspectives in bronchiectasis management
• Compassionate use trials and equitable access to variant-specific treatment for cystic fibrosis
• Compound heterozygous CFTR variants (Q1352H and 5T; TG13) in a Chinese patient with cystic fibrosis
• Cross-cultural adaptation and validation of the CFAbd-Score for gastrointestinal symptoms in patients with cystic fibrosis
• Cystic fibrosis
• Cystic fibrosis dermatitis arthritis syndrome: A series of four cases
• Cystic fibrosis transition from paediatric to adult care: international survey results
• Cystic fibrosis-related chronic rhinosinusitis: the key role of a comprehensive evaluation in the era of highly effective modulator therapy
• Cystic fibrosis-related diabetes develops from a combination of insulin secretion defects and insulin resistance
• Death in a bathtub of an adolescent with neurofibromatosis type 2 exhibiting meningioangiomatosis with white matter involvement
• Definitions of pulmonary exacerbation in people with cystic fibrosis: a scoping review
• Description and first insights on a large genomic biobank of lung transplantation
• Detection of the epidemic Pseudomonas aeruginosa AUST-03 (ST242) strain in people with cystic fibrosis in South Africa
• Development and validation of a novel questionnaire to describe and assess sensations and triggers associated with refractory and unexplained chronic cough
• Diagnostic value of serum vascular endothelial growth factor-D in Korean patients with lymphangioleiomyomatosis
• Dysfunctional mucus structure in cystic fibrosis increases vulnerability to colibactin-mediated DNA adducts in the colon mucosa
• Editorial: Cystic fibrosis-related diabetes
• Epidemiology of advanced cystic fibrosis lung disease in the modulator era
• Genome-Wide Association Study of Susceptibility to Pseudomonas aeruginosa Infection in Cystic Fibrosis
• Gut epithelial electrical cues drive differential localization of enterobacteria
• Imaging findings of thoracic manifestations of Crohn's disease and ulcerative colitis
• Impact of day-to-day variation in FEV1 on measures of change: A conceptual description
• Impaired Glucose Metabolism, Primary Cilium Defects, and Kidney Cystogenesis in Glycogen Storage Disease Type Ia
• Improved detection of mycobacteria in CF and tissue samples grown in mycobacteria growth indicator tube incubated at 30°C compared to conventional growth conditions of liquid and solid media
• In a sticky situation: Pro-coagulant properties expand the importance of neutrophil EVs in driving tissue injury
• Inhalation of SP-101 followed by inhaled doxorubicin results in robust and durable hCFTRdeltaR transgene expression in the airways of wild-type and cystic fibrosis ferrets
• Inhaled Nanoparticulate Systems: Composition, Manufacture and Aerosol Delivery
• Innovative all-in-one exome sequencing strategy for diagnostic genetic testing in male infertility: Validation and 10-month experience
• INSIGHTS INTO THE ORIGINS OF CYSTIC FIBROSIS LUNG DISEASE
• Is sweat conductivity still a relevant screening test for cystic fibrosis? Participation over 10 years
• Literary evidence of the impact of nonbiological risk factors on CRMS/CFSPID: A scoping review
• Long-distance microbial mechanisms impacting cancer immunosurveillance
• Long-Term Impact of Lumacaftor/Ivacaftor Treatment on Cystic Fibrosis Disease Progression in Children 2 Through 5 Years of Age Homozygous for F508del-CFTR: A Phase 2, Open-Label Clinical Trial
• Lung transplant referral considerations for individuals with cystic fibrosis
• Medication adherence to CFTR modulators in patients with cystic fibrosis: a systematic review
• Metabolic alkalosis in cystic fibrosis: from vascular volume depletion to impaired bicarbonate excretion
• Metabolic specialization drives reduced pathogenicity in Pseudomonas aeruginosa isolates from cystic fibrosis patients
• Mood Swings and Irritability in a Patient With Cystic Fibrosis on Elexacaftor-Tezacaftor-Ivacaftor Therapy: A Case Report
• mSphere of Influence: The power of polymicrobial partnerships in chronic infection research
• Nasal High-Flow Oxygen Therapy in Chronic Respiratory Failure for Homecare Applications-A Feasibility Study
• Outcomes in Black People with Cystic Fibrosis: A Registry Analysis
• Overnutrition in persons with cystic fibrosis on modulator therapy and the relationship to obstructive sleep apnea
• Pancreatic Crosstalk in the Disease Setting: Understanding the Impact of Exocrine Disease on Endocrine Function
• PANoptosis opens new treatment options for allergic bronchopulmonary aspergillosis
• Phage Therapy: An Alternative Approach to Combating Multidrug-Resistant Bacterial Infections in Cystic Fibrosis
• Pharmacological and pre-clinical safety profile of rSIV.F/HN, a hybrid lentiviral vector for cystic fibrosis gene therapy
• Phase-resolved MRI for measurement of pulmonary perfusion and ventilation defects in comparison with dynamic contrast-enhanced MRI and ¹²⁹Xe MRI
• PM_2.5 Exposure Inhibits Transepithelial Anion Short-circuit Current by Downregulating P2Y2 Receptor/CFTR Pathway
• Potential of extracellular vesicles in the pathogenesis, diagnosis and therapy for parasitic diseases
• Practical Guidance for Clinical Microbiology Laboratories: Updated guidance for processing respiratory tract samples from people with cystic fibrosis
• Premodulator microbiome alterations associated with postmodulator growth outcomes in pediatric cystic fibrosis: Can we predict outcomes?
• Prevalence of psychotropic medication dispensing to people living with cystic fibrosis in Australia: 2013-2022
• Profiling severe asthma: Any relevance for age? An analysis from Severe Asthma Network Italy (SANI) cohort
• Prospective Analysis of urINe LAM to Eliminate NTM Sputum Screening (PAINLESS) study: Rationale and trial design for testing urine lipoarabinomannan as a marker of NTM lung infection in cystic fibrosis
• Rare host variants in ciliary expressed genes contribute to COVID-19 severity in Bulgarian patients
• Robust identification of environmental exposures and community characteristics predictive of rapid lung disease progression
• Salivary proteomic signatures in severe dental fluorosis
• ScyNet: Visualizing interactions in community metabolic models
• Secondary immunodeficiency and non-cystic fibrosis bronchiectasis
• Secondary use of patient data within decentralized studies using the example of rare diseases in Germany: A data scientist's exploration of process and lessons learned
• Silence of the lungs: comparing measures of slow and non-communicating lung units from pulmonary function tests with computed tomography
• Socioeconomic burden of cystic fibrosis in Canada
• SP-101, a novel adeno-associated virus gene therapy for the treatment of cystic fibrosis, mediates functional correction of primary human airway epithelia from donors with cystic fibrosis
• Sputum proteomics in lung disorders
• Stellate cells are in utero markers of pancreatic disease in cystic fibrosis
• Synthesis and Biological Evaluation of Pyrazole-Pyrimidones as a New Class of Correctors of the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR)
• The clinical, economic, and humanistic burden of treatments for exocrine pancreatic insufficiency and cost-effectiveness of treatments: A systematic literature review
• The continuing need for dornase alfa for extracellular airway DNA hydrolysis in the era of CFTR modulators
• The Coronavirus Disease 2019 Pandemic and Time to Diagnosis for Childhood Pulmonary Diseases: Outcomes of a Tertiary Care Center
• The diversity of clinical <em>Mycobacterium abscessus</em> isolates in morphology, glycopeptidolipids and infection rates in a macrophage model
• The effects of airway disease on the deposition of inhaled drugs
• The expanded French compassionate programme for elexacaftor-tezacaftor-ivacaftor use in people with cystic fibrosis without a F508del CFTR variant: a real-world study
• The L-lactate dehydrogenases of <em>Pseudomonas aeruginosa</em> are conditionally regulated but both contribute to survival during macrophage infection
• Towards improved biofilm models
• Tradeoffs Between Evolved Phage Resistance and Antibiotic Susceptibility in a Highly Drug-Resistant Cystic Fibrosis-Derived Pseudomonas aeruginosa Strain
• Transcriptome analyses reveal key features of mouse seminal vesicle during aging
• Type 2 asthma paediatric patients eligible for dupilumab: An Italian biomarker-based analysis
• Understanding the physical literacy development of 8- to 12-year-old children living with chronic medical conditions: A comprehensive, mixed methods inquiry
• Update on the Role of Chest Imaging in Cystic Fibrosis