Disease: Cystic fibrosis
- <em>Pseudomonas aeruginosa</em> Lipid A Structural Variants Induce Altered Immune Responses
- "Therapeutic improvement of CFTR function and reversibility of bronchiectasis in cystic fibrosis." M.O. Wielputz and M.A. Mall. Eur Respir J 2024; 63: 2400234
- "We'll deal with it as it comes": A Qualitative Analysis of Romantic Partners' Dyadic Coping in Cystic Fibrosis
- A case of phyllodes tumor with rapid growth during pregnancy and lactation period: a case report
- A new era of targeting cystic fibrosis with non-viral delivery of genomic medicines
- A promoter-dependent upstream activator augments CFTR expression in diverse epithelial cell types
- A systematic review of animal and human data comparing the nasal potential difference test between cystic fibrosis and control
- AAV-vectored expression of monospecific or bispecific monoclonal antibodies protects mice from lethal Pseudomonas aeruginosa pneumonia
- Altered serine metabolism promotes drug tolerance in <em>Mycobacterium abscessus</em> via a WhiB7-mediated adaptive stress response
- An Overview of Frog Skin-Derived Esc Peptides: Promising Multifunctional Weapons against <em>Pseudomonas aeruginosa</em>-Induced Pulmonary and Ocular Surface Infections
- Attitudes to cross infection, nebuliser hygiene and antimicrobial resistance in people with cystic fibrosis: Results of an international survey
- Author Correction: Fungal Colonization of the Airways of Patients with Cystic Fibrosis: The Role of the Environmental Reservoirs
- Bronchiectasis not due to cystic fibrosis
- Case Report: When cystic fibrosis, elexacaftor/tezacaftor/ivacaftor therapy, and alpha1 antitrypsin deficiency get together
- Case Series: Efficacy of Polyclonal Intravenous Immunoglobulin for Refractory <em>Clostridioides difficile</em> Infection
- Changes in urinary glutathione sulfonamide (GSA) levels between admission and discharge of patients with cystic fibrosis
- Chloride/Multiple Anion Exchanger SLC26A Family: Systemic Roles of SLC26A4 in Various Organs
- Ciliopathy patient variants reveal organelle-specific functions for TUBB4B in axonemal microtubules
- Concentrations of dehydroepiandrosterone-sulphate (DHEA-S) in people with cystic fibrosis on and off elexacaftor-tezacaftor-ivacaftor
- Could the HALP score serve as a biomarker of bronchiectasis exacerbation?
- Cystic fibrosis in Iceland and the high prevalence of the N1303K variant
- Cystic fibrosis newborn screening in Switzerland - evaluation and scenarios for improvement after 11 years of follow-up
- Durable transgene expression and efficient re-administration after rAAV2.5T-mediated fCFTRΔR gene delivery to adult ferret lungs
- Echinococcus granulosus ubiquitin-conjugating enzymes (E2D2 and E2N) promote the formation of liver fibrosis in TGFbeta1-induced LX-2 cells
- Echocardiographic assessment of cardiovascular involvements in children with cystic fibrosis
- Effects of donor smoking history on early post-transplant lung function measured by oscillometry
- Efficacy and safety of a new low-volume PEG with citrate and simethicone bowel preparation for pediatric elective colonoscopy: Phase 3 RCT
- Elexacaftor/tezacaftor/ivacaftor influences body composition in adults with cystic fibrosis: a fully automated CT-based analysis
- Epidemiology, microbiological, clinical characteristics, and outcome of Burkholderia cepacia complex infections in non-cystic fibrosis adult patients from Qatar
- Evaluating the potential of daily intake of polystyrene microplastics via drinking water in inducing PCOS and its ovarian fibrosis progression using female zebrafish
- Evaluation of mixed biofilm production by Candida spp. and Staphylococcus aureus strains co-isolated from cystic fibrosis patients in northwest Algeria
- Evolution of nutritional management in children with cystic fibrosis - a narrative review
- Evolution of Resistance against Ciprofloxacin, Tobramycin, and Trimethoprim/Sulfamethoxazole in the Environmental Opportunistic Pathogen <em>Stenotrophomonas maltophilia</em>
- Exploring the link between a novel approach for computer aided lung sound analysis and imaging biomarkers: a cross-sectional study
- Five-Year Outcomes Among U.S. Bronchiectasis and Nontuberculous Mycobacterial Registry Patients
- Generation of human-induced pluripotent stem cells from a patient with homozygous I1234V mutation of cystic fibrosis
- Genetic determinants of antimicrobial resistance in polymyxin B resistant Pseudomonas aeruginosa isolated from airways of patients with cystic fibrosis
- Genome-scale model of <em>Rothia mucilaginosa</em> predicts gene essentialities and reveals metabolic capabilities
- Global incidence, prevalence, years lived with disability (YLDs), disability-adjusted life-years (DALYs), and healthy life expectancy (HALE) for 371 diseases and injuries in 204 countries and territories and 811 subnational locations, 1990-2021: a systema
- How Does Airway Surface Liquid Composition Vary in Different Pulmonary Diseases, and How Can We Use This Knowledge to Model Microbial Infections?
- Imaging features and surgical management of giant parathyroid adenoma with autoinfarction
- Impact of CFTR modulator therapy on body composition as assessed by thoracic computed tomography: A follow-up study
- Impact of Pseudomonas aeruginosa on resource utilization and costs in patients with exacerbated non-cystic fibrosis bronchiectasis
- In utero and postnatal ivacaftor/lumacaftor therapy rescues multiorgan disease in CFTR-F508del ferrets
- In vitro platform to model the function of ionocytes in the human airway epithelium
- Inquilinus limosus, an atypical Gram-negative rod from lung transplant recipients and cystic fibrosis patients
- Insights on Pseudomonas aeruginosa Carbohydrate Binding from Profiles of Cystic Fibrosis Isolates Using Multivalent Fluorescent Glycopolymers Bearing Pendant Monosaccharides
- International Perspectives of Extended Genetic Sequencing When Used as Part of Newborn Screening to Identify Cystic Fibrosis
- Invited Commentary regarding Manuscript JLR-D-23-00602R1. Revised title 'Fatty acid malabsorption followed by chylomicron malformation, not pancreatic insufficiency, cause metabolic defects in cystic fibrosis', by Teng L et al
- Labeling of Mucin-Type <em>O</em>-Glycans for Quantification Using Liquid Chromatography and Fluorescence Detection
- Leveraging Large Language Models to Analyze Continuous Glucose Monitoring Data: A Case Study
- Ligand-based virtual-screening identified a novel CFTR ligand which improves the defective cell surface expression of misfolded ABC transporters
- Lipoarabinomannan modification as a source of phenotypic heterogeneity in host-adapted <em>Mycobacterium abscessus</em> isolates
- Liposomes for Inhalation
- Longitudinal improvements in clinical and functional outcomes following initiation of elexacaftor/tezacaftor/ivacaftor in patients with cystic fibrosis
- Lung Donor Bronchoalveolar Lavage Positivity: Incidence, Risk Factors, and Lung Transplant Recipients' Outcome
- Lytic bacteriophages induce the secretion of antiviral and proinflammatory cytokines from human respiratory epithelial cells
- Monoclonal antibodies derived from B cells in subjects with cystic fibrosis reduce Pseudomonas aeruginosa burden in mice
- Mutational spectrum of CFTR in cystic fibrosis patients with gastrointestinal and hepatobiliary manifestations
- Neutrophil Elastase Degrades Histone Deacetylases and Sirtuin 1 in Primary Human Monocyte Derived Macrophages
- Neutrophil Extracellular Traps and Respiratory Disease
- Newborn screening in France: news and perspectives
- Novel <em>Ralstonia</em> species from human infections: improved matrix-assisted laser desorption/ionization time-of-flight mass spectrometry-based identification and analysis of antimicrobial resistance patterns
- Novel Dry Hyaluronic Acid-Vancomycin Complex Powder for Inhalation, Useful in Pulmonary Infections Associated with Cystic Fibrosis
- Overcoming Burkholderia cepacia by successful eradication with clinical improvement in cystic fibrosis
- Pancreatic enzymes digest obstructive meconium from cystic fibrosis pig intestines
- Parental perceptions of body weight and appetite in infants and toddlers with cystic fibrosis
- Pathophysiology of non-cystic fibrosis bronchiectasis in children and adolescents with asthma: A protocol for systematic review and meta-analysis
- Porcine-derived pancreatic enzyme replacement therapy may be linked to chronic hepatitis E virus infection in cystic fibrosis lung transplant recipients
- Predicting lung function decline in cystic fibrosis: the impact of initiating ivacaftor therapy
- Predictors of Sinonasal Improvement After Highly Effective Modulator Therapy in Adults with Cystic Fibrosis
- Presentation, characteristics and management of obstructive intestinal conditions in cystic fibrosis
- Prevention of RSV Bronchiolitis: An Ethical Issue
- Prognostic Significance of NLR and PLR in COVID-19: A Multi-Cohort Validation Study
- Pulmonary function and body composition parameters of children with cystic fibrosis from a hight complexity institution between 2015 and 2018
- Radiographic Outcomes in Paediatric Bronchiectasis and Factors Associated with Reversibility
- Recessively Inherited Deficiency of Secreted WFDC2 (HE4) Causes Nasal Polyposis and Bronchiectasis
- Recommended Tool Compounds for Modifying the Cystic Fibrosis Transmembrane Conductance Regulator Channel Variants
- Reply to Kebui R and Emiroglu HH
- Risk Factors for Complications and Disease Recurrence after Ileocecal Resection for Crohn's Disease in Children and Adults
- Secondary messenger signalling influences Pseudomonas aeruginosa adaptation to sinus and lung environments
- Secondary metabolite profiling of <em>Pseudomonas aeruginosa</em> isolates reveals rare genomic traits
- Septin-dependent defense mechanisms against Pseudomonas aeruginosa are stalled in cystic fibrosis bronchial epithelial cells
- SERS Microsensors for the Study of pH Regulation in Cystic Fibrosis Patient-Derived Airway Cultures
- Short-term azithromycin use is associated with QTc interval prolongation in children with cystic fibrosis
- Sinapic acid modulates oxidative stress and metabolic disturbances to attenuate ovarian fibrosis in letrozole-induced polycystic ovary syndrome SD rats
- Substituted 4H-3,1-benzoxazine-4-one Derivatives as Inhibitors of Cathepsin G
- Successful management of Mycobacterium abscessus pneumonia in a 53-day-old immunocompetent infant
- Surface-Exposed Protein Moieties of <em>Burkholderia cenocepacia</em> J2315 in Microaerophilic and Aerobic Conditions
- The anoctamins: Structure and function
- The changing epidemiology of pulmonary infection in children and adolescents with cystic fibrosis: an 18-year experience
- The effect of respiratory muscle training on children and adolescents with cystic fibrosis: a systematic review and meta-analysis
- The folding pathway of ABC transporter CFTR: effective and robust
- The role of Staphylococcus aureus in cystic fibrosis pathogenesis and clinico-microbiological interactions
- The role of volatile organic compounds for assessing characteristics and severity of non-cystic fibrosis bronchiectasis: an observational study
- Two-Year Impact of Highly Effective Modulator Therapy on Olfactory Dysfunction
- Ultra-fast<em>in-vivo</em>directional dark-field x-ray imaging for visualising magnetic control of particles for airway gene delivery
- Understanding advanced cystic fibrosis liver disease through genetic variation: Where do the pathways lead and how much further must we go?
- Update on the diagnosis and management of cystic fibrosis pulmonary exacerbations
- Why Certain Repurposed Drugs Are Unlikely to Be Effective Antivirals to Treat SARS-CoV-2 Infections