• A case of cholangitis-type congenital hepatic fibrosis due to a mutation in the polycystic kidney/hepatic disease 1 gene
• A case of congenital hepatic fibrosis diagnosed and treated by transjugular intrahepatic portosystemic shunt
• A case of neonatal liver failure
• A clinical review of congenital hepatic fibrosis diagnosed in adulthood: presentation, complications, and outcomes
• A discarded synonymous variant in NPHP3 explains nephronophthisis and congenital hepatic fibrosis in several families
• A pregnant woman with congenital hepatic fibrosis delivers a healthy neonate
• A Rare Case Mimicking Congenital Hepatic Fibrosis
• A Rare Cause of Liver Fibrosis in Adulthood
• AN 84-YEAR-OLD PATIENT WITH CAROLI SYNDROME: WHAT IS THE PROGNOSIS OF THIS CONDITION?
• An update on ductal plate malformations and fibropolycystic diseases of the liver
• Apixaban Causing Hepatic Cystic Bleeding: A Rare but a Life-Threatening Complication
• Association between congenital heart disease and parenteral nutrition-associated liver disease in neonates: A retrospective cohort study
• Association of congenital hepatic fibrosis and Caroli's syndrome: Two illustrative cases
• Association of novel TMEM67 variants with mild phenotypes of high gamma-glutamyl transpeptidase cholestasis and congenital hepatic fibrosis
• Associations of Liver Stiffness Measured by Ultrasound Shear-Wave Elastography With Portal Hypertension and Circulatory Failure in Individuals With Fontan Circulation
• Autosomal Recessive Polycystic Kidney Disease
• Autosomal Recessive Polycystic Kidney Disease-The Clinical Aspects and Diagnostic Challenges
• Autosomal Recessive Polycystic Kidney Disease: Diagnosis, Prognosis, and Management
• Biallelic loss-of-function ZFYVE19 mutations are associated with congenital hepatic fibrosis, sclerosing cholangiopathy and high-GGT cholestasis
• Biliary sepsis complication with congenital hepatic fibrosis: an unexpected outcome
• Biomarkers for liver disease in urea cycle disorders
• Brucella Peritonitis in a Patient on Peritoneal Dialysis: A Case Report and Review of Literature
• Care Pattern for Fontan-Associated Liver Disease by Academic Pediatric Hepatologists in Canada
• Caroli Disease
• Caroli Disease
• Caroli disease with subcutaneous hemorrhage as the sole clinical manifestation: A case report
• Caroli syndrome associated with atrial septal defect and polydactyly: a case report
• Caroli's disease incidentally discovered in a 16-years-old female: a case report
• Caroli's Syndrome: A Case Report and Literature Review
• Caroli's Syndrome: An Early Presentation
• Case report: Rare genetic liver disease - a case of congenital hepatic fibrosis in adults with autosomal dominant polycystic kidney disease
• Chyloperitoneum After Penetrating Abdominal Trauma: A Report of a Rare Case
• Clinical and invasively-measured predictors of high exercise capacity in Fontan patients
• Clinical and pathological features of 20 cases of congenital hepatic fibrosis
• Clinical Outcomes of Adult Fontan-Associated Liver Disease and Combined Heart-Liver Transplantation
• Clinicopathological features of congenital hepatic fibrosis
• Combined liver-kidney transplantation in pediatric patients
• Congenital hepatic fibrosis and its mimics: a clinicopathologic study of 19 cases at a single institution
• Congenital Hepatic Fibrosis as an Early Sign of Presentation of ADPKD
• Congenital Hepatic Fibrosis in a 2-Year-Old Child Presenting with Fever of Unknown Origin
• Congenital hepatic fibrosis in a young boy with congenital hypothyroidism: A case report
• Congenital Hepatic Fibrosis in Children and Adults: Clinical Manifestations, Management, and Outcome-Case Series and Literature Review
• Congenital Hepatic Fibrosis Presenting With Pancytopenia
• Congenital hepatic fibrosis with negative endoscopic evaluation of esophageal and gastric varices: A case report
• Congenital hepatic fibrosis: case report and review of literature
• Diffuse Versus Localized Caroli Disease: A Comparative MRCP Study
• Dysregulation of the Scribble/YAP/beta-catenin axis sustains the fibroinflammatory response in a PKHD1(-/-) mouse model of congenital hepatic fibrosis
• Dysregulation of the Scribble/YAP/β-catenin axis sustains the fibroinflammatory response in a PKHD1^-/- mouse model of congenital hepatic fibrosis
• Early clinical management of autosomal recessive polycystic kidney disease
• Elderly onset congenital hepatic fibrosis with portal hypertension diagnosed after recurrent cholangitis: a case report
• Esophagogastric variceal bleeding as a debut of Caroli's syndrome
• Evaluation of galectin-3 and intestinal fatty acid binding protein as serum biomarkers in autosomal recessive polycystic kidney disease
• Fetal congenital gastrointestinal obstruction: prenatal diagnosis of chromosome microarray analysis and pregnancy outcomes
• Fibrocystic liver disease: novel concepts and translational perspectives
• Global Transcriptomics of Congenital Hepatic Fibrosis in Autosomal Recessive Polycystic Kidney Disease using PCK rats
• Heritable Chronic Cholestatic Liver Diseases: A Review
• Histopathology and molecular pathology confirmed a diagnosis of atypical Caroli's syndrome: a case report
• Identification of differentially expressed long noncoding RNAs and pathways in liver tissues from rats with hepatic fibrosis
• Imaging of fibropolycystic liver disease
• Inflammatory pathways and cholangiocarcinoma risk mechanisms and prevention
• Intrahepatic transcriptomics differentiate advanced fibrosis and clinical outcomes in adults with the Fontan circulation
• Issues in multi-organ transplantation of the liver with kidney or heart in polycystic liver-kidney disease or congenital heart disease: Current practices and immunological aspects
• Kidney Transplant and Autosomal Recessive Polycystic Disease: A Case Report and Literature Review of 2 Brothers
• Liver Fibrosis Markers Represent Central Venous Pressure in Post-pubertal Patients With Congenital Heart Disease
• Liver Graft Failure after Plastic Stent Removal of an Anastomotic Biliary Stricture
• Liver transplantation for congenital hepatic fibrosis
• Liver-specific DICER1 syndrome model mice develop cystic liver tumors with defective primary cilia
• Long term outcome of MPI-CDG patients on D-mannose therapy
• Long-term kidney and liver outcome in 50 children with autosomal recessive polycystic kidney disease
• Loss of Anks6 leads to YAP deficiency and liver abnormalities
• Magnetic resonance elastography to quantify liver disease severity in autosomal recessive polycystic kidney disease
• Mannose phosphate isomerase gene mutation leads to a congenital disorder of glycosylation: A rare case report and literature review
• Mitigation of portal fibrosis and cholestatic liver disease in ANKS6-deficient livers by macrophage depletion
• Multiple hepatocyte nuclear factor 1A (HNF1A)-inactivated hepatocellular adenomas arising in a background of congenital hepatic fibrosis
• Nephronophthisis 13 caused by WDR19 variants with pancytopenia: case report
• Notch-Hes1 signaling activation in Caroli disease and polycystic liver disease
• Organ Abnormalities Caused by Turner Syndrome
• Outcomes of Combined Liver-Kidney Transplantation - Single Center Experience
• Pediatric Cholestatic Liver Disease: Review of Bile Acid Metabolism and Discussion of Current and Emerging Therapies
• Pediatric non-cirrhotic portal hypertension: Endoscopic outcome and perspectives from developing nations
• Performance and Interpretation of Clot Waveform Analysis
• Pleural Kaposi sarcoma: an unusual clinical case
• Portal Steal Syndrome From a Large Linton's Splenorenal Shunt after Liver Transplantation: Successful Endovascular Management Through Off-Label Application of a 30 mm Amplatzer Cardiac Plug
• Prospective evaluation of kidney and liver disease in autosomal recessive polycystic kidney disease-congenital hepatic fibrosis
• Pulsatile Epigastric Mass and Liver Masses in a 38-Year-Old Patient With Splenomegaly Since Childhood
• Rare variants in PKHD1 associated with Caroli syndrome: Two case reports
• Relationships between congenital peritoneopericardial diaphragmatic hernia or congenital central diaphragmatic hernia and ductal plate malformations in dogs and cats
• Retraction: Protein kinase a-dependent pSer 675 -beta-catenin, a novel signaling defect in a mouse model of congenital hepatic fibrosis
• Retraction: Protein kinase a-dependent pSer 675 -β-catenin, a novel signaling defect in a mouse model of congenital hepatic fibrosis
• Retraction: Protein kinase a-dependent pSer675-β-catenin, a novel signaling defect in a mouse model of congenital hepatic fibrosis
• Right hepatectomy with a cholangiojejunostomy and hepaticojejunostomy for unilobar Caroli's syndrome
• Surgical technique and the long-term outcomes of pediatric living donor domino liver transplantation from patients with maple syrup urine disease
• Suspected Autosomal Recessive Polycystic Kidney Disease but Cerebellar Vermis Hypoplasia, Oligophrenia Ataxia, Coloboma, and Hepatic Fibrosis (COACH) Syndrome in Retrospect, A Delayed Diagnosis Aided by Genotyping and Reverse Phenotyping: A Case Report an
• The Ductal Plate From the Inside Out: An Illustrated Review of Fibropolycystic Liver Disease
• The genetic spectrum of polycystic kidney disease in children
• The role of liver transplantation in COACH syndrome (Joubert syndrome with congenital hepatic fibrosis): A review of the literature
• Transjugular intrahepatic portosystemic shunt for portal hypertension in a patient with Caroli disease
• Two cases of DCDC2-related neonatal sclerosing cholangitis with developmental delay and literature review
• Two-dimensional (2D) morphologic measurements can quantify the severity of liver disease in children with autosomal recessive polycystic kidney disease (ARPKD)
• Variable Clinical Presentations and Renal Outcome in Neonates With Autosomal Recessive Polycystic Kidney Disease