• A Novel De Novo Missense Mutation in KIF1A Associated with Young-Onset Upper-Limb Amyotrophic Lateral Sclerosis
• A patient-derived amyotrophic lateral sclerosis blood-brain barrier model for focused ultrasound-mediated anti-TDP-43 antibody delivery
• Abnormal Splicing Events due to Loss of Nuclear Function of TDP-43: Pathophysiology and Perspectives
• All-in-one wearable drug efficacy assessment systems for bulbar muscle function using amyotrophic lateral sclerosis animal models
• Allele-Selective Thiomorpholino Antisense Oligonucleotides as a Therapeutic Approach for Fused-in-Sarcoma Amyotrophic Lateral Sclerosis
• ALS-FUS mutations cause abnormal PARylation and histone H1.2 interaction, leading to pathological changes
• Amyotrophic Lateral Sclerosis (ALS): An Overview of Genetic and Metabolic Signaling Mechanisms
• Amyotrophic lateral sclerosis associated with a new pathogenic variant of the ERBB4 gene
• An Accurate and Rapidly Calibrating Speech Neuroprosthesis
• An automatic measure for speech intelligibility in dysarthrias-validation across multiple languages and neurological disorders
• Anesthetic Management of a Neurosurgical Patient With Amyotrophic Lateral Sclerosis: A Case Report
• Brain-Computer Interfaces for Restoring Communication
• Bulbar muscle impairment in patients with late onset Pompe disease: Insight from the French Pompe registry
• Causal relationship between imaging-derived phenotypes and neurodegenerative diseases: a Mendelian randomization study
• Central neurodegeneration in Kennedy's disease accompanies peripheral motor dysfunction
• CHCHD2 P14L, found in amyotrophic lateral sclerosis, exhibits cytoplasmic mislocalization and alters Ca(2+) homeostasis
• Circulating endocannabinoidome signatures of disease activity in amyotrophic lateral sclerosis
• Circulating MAIT cells in multiple sclerosis and amyotrophic lateral sclerosis
• Clinical characterization of common pathogenic variants of SOD1-ALS in Germany
• Coffee and amyotrophic lateral sclerosis (ALS)
• Coffee, antioxidants, and brain inflammation
• Comparative assessment of MScanFit MUNE and quantitative EMG in amyotrophic lateral sclerosis diagnosis: A prospective study
• Compassionate Ventilator Release in Patients With Neuromuscular Disease: A Two-Case Comparison
• Cortical inexcitability in ALS: correlating a clinical phenotype
• Cortical microstructural abnormalities in amyotrophic lateral sclerosis: a gray matter-based spatial statistics study
• CSF Neopterin Levels Are Elevated in Various Neurological Diseases and Aging
• Current progress in microRNA profiling of circulating extracellular vesicles in amyotrophic lateral sclerosis: A systematic review
• Current status and new avenues of stem cell-based preclinical and therapeutic approaches in amyotrophic lateral sclerosis
• D-Glutamate production by stressed Escherichia coli gives a clue for the hypothetical induction mechanism of the ALS disease
• Data and Process Harmonisation of Multi-National, Multi-Site Research Data
• Development and Piloting of a Bereaved Care Partner Survey to Inform Quality Improvement in ALS Supportive Care
• Diagnostic elements in amyotrophic lateral sclerosis: A case report
• Different baseline functional patterns of the frontal cortex in amyotrophic lateral sclerosis patients with Corticospinal tract hyperintensity
• Dilemma in patients with amyotrophic lateral sclerosis and expectations from brain-machine interfaces
• Diverse Phenotypic Presentation of the Welander Distal Myopathy Founder Mutation, With Myopathy and Amyotrophic Lateral Sclerosis in the Same Family
• DNAJA2 and Hero11 mediate similar conformational extension and aggregation suppression of TDP-43
• Electrodiagnostic support in an atypical form of amyotrophic lateral sclerosis (Vulpian-Bernhardt syndrome)
• Electrografted Laser-Induced Graphene: Direct Detection of Neurodegenerative Disease Biomarker in Cerebrospinal Fluid
• Excitotoxicity, Oxytosis/Ferroptosis, and Neurodegeneration: Emerging Insights into Mitochondrial Mechanisms
• Exploring the Impact of Amyotrophic Lateral Sclerosis on Otolaryngological Functions
• Factors associated with Edinburgh Cognitive and Behavioural ALS Screen (ECAS) alteration at time of diagnosis, in amyotrophic lateral sclerosis
• Fatty links between multisystem proteinopathy and small VCP-interacting protein
• Friend or foe: Lactate in neurodegenerative diseases
• Genotype-phenotype correlation of SQSTM1 variants in patients with amyotrophic lateral sclerosis
• Harnessing transcriptomic signals for amyotrophic lateral sclerosis to identify novel drugs and enhance risk prediction
• HDAC6 inhibition as a mechanism to prevent neurodegeneration in the mSOD1^G93A mouse model of ALS
• Identification of human metabolites of fast skeletal troponin activators Tirasemtiv and Reldesemtiv for doping control purposes
• Identification of potential drug targets for amyotrophic lateral sclerosis by Mendelian randomization analysis based on brain and plasma proteomics
• Inhibition of glycolytic reprogramming suppresses innate immune-mediated inflammation in experimental amyotrophic lateral sclerosis
• Inhibition of PHLDA3 expression in human superoxide dismutase 1-mutant amyotrophic lateral sclerosis astrocytes protects against neurotoxicity
• Intranasal delivery of small extracellular vesicles reduces the progress of amyotrophic lateral sclerosis and the overactivation of complement-coagulation cascade and NF-qB signaling in SOD1(G93A) mice
• Klotho: molecular mechanisms and emerging therapeutics in central nervous system diseases
• Lingual Fasciculation as a Point of Call for the Diagnosis of Amyotrophic Lateral Sclerosis: A Literature Review
• Longevity of a Brain-Computer Interface for Amyotrophic Lateral Sclerosis
• Low-intensity pulsed ultrasound modulates disease progression in the SOD1(G93A) mouse model of amyotrophic lateral sclerosis
• LPA3 agonist-producing Bacillus velezensis ADS024 is efficacious in multiple neuroinflammatory disease models
• Mass spectrometry imaging of SOD1 protein-metal complexes in SOD1G93A transgenic mice implicates demetalation with pathology
• Mitochondrial Dysfunction is a Crucial Immune Checkpoint for Neuroinflammation and Neurodegeneration: mtDAMPs in Focus
• Mitochondrial genome variants associated with amyotrophic lateral sclerosis and their haplogroup distribution
• Molecular mechanisms and antisense oligonucleotide therapies of familial amyotrophic lateral sclerosis
• Morphometric analysis of spinal motor neuron degeneration in sporadic amyotrophic lateral sclerosis
• Multimodal speech biomarkers for remote monitoring of ALS disease progression
• Multiple metal exposures associate with higher amyotrophic lateral sclerosis risk and mortality independent of genetic risk and correlate to self-reported exposures: a case-control study
• Novel multitarget directed ligands inspired by riluzole: A serendipitous synthesis of substituted benzo[b][1,4]thiazepines potentially useful as neuroprotective agents
• Overexpression of Toxic Poly(Glycine-Alanine) Aggregates in Primary Neuronal Cultures Induces Time-Dependent Autophagic and Synaptic Alterations but Subtle Activity Impairments
• Patient-Reported Impact of Symptoms in Spinal and Bulbar Muscular Atrophy
• Physical exercise in amyotrophic lateral sclerosis: a potential co-adjuvant therapeutic option to counteract disease progression
• Poly-GR Impairs PRMT1-Mediated Arginine Methylation of Disease-Linked RNA-Binding Proteins by Acting as a Substrate Sink
• Poly-GR repeats associated with ALS/FTD gene <em>C9ORF72</em> impair translation elongation and induce a ribotoxic stress response in neurons
• Population-Based Evidence for the Use of Serum Neurofilaments as Individual Diagnostic and Prognostic Biomarkers in Amyotrophic Lateral Sclerosis
• Postmovement Beta Rebound in Real and Imagined Movement
• Promising animal models for amyotrophic lateral sclerosis drug discovery: a comprehensive update
• Prostaglandins in the Inflamed Central Nervous System: Potential Therapeutic Targets
• Psychiatric Manifestations of Neurological Diseases: A Narrative Review
• RBM5 induces motor neuron apoptosis in hSOD1(G93A)-related amyotrophic lateral sclerosis by inhibiting Rac1/AKT pathways
• Schwann cell JUN expression worsens motor performance in an amyotrophic lateral sclerosis mouse model
• Scientific plurality and amyotrophic lateral sclerosis (ALS): A philosophical and historical perspective on Charcot's texts
• Sigma-1 receptor recruits LC3 mRNA to ER-associated omegasomes to promote localized LC3 translation enabling functional autophagy
• Simultaneous time-frequency analysis of gait signals of both legs in classifying neurodegenerative diseases
• Small Molecule Inhibitors of Arylamine N-Acetyltransferase 1 Attenuate Cellular Respiration
• SoDCoD: a comprehensive database of Cu/Zn superoxide dismutase conformational diversity caused by ALS-linked gene mutations and other perturbations
• Sonography of muscles : Rheumatology-Neurology-Geriatrics-Sports medicine-Orthopedics
• Stress granule formation helps to mitigate neurodegeneration
• Structural basis for RNA recognition by the C-terminal RRM domain of human RBM45
• TBK1 p.Y153Qfs*9 variant may be associated with young-onset, rapidly progressive amyotrophic lateral sclerosis through a haploinsufficiency mechanism
• TDP-43 dysfunction leads to bioenergetic failure and lipid metabolic rewiring in human cells
• The ALS-associated KIF5A P986L variant is not pathogenic for Drosophila motoneurons
• The Evolving Use of Gold Nanoparticles as a Possible Reversal Agent for the Symptoms of Neurodegenerative Diseases: A Narrative Review
• The prion-like effect and prion-like protein targeting strategy in amyotrophic lateral sclerosis
• The role of biomolecular condensates in protein aggregation
• The role of interferon beta in neurological diseases and its potential therapeutic relevance
• The role of macrophage plasticity in neurodegenerative diseases
• The speed of completion of the decremental responses on repetitive nerve stimulation
• Timeline of hypoglossal motor neuron death and intrinsic tongue muscle denervation in high-copy number SOD1^G93A mice
• Unlocking the therapeutic potential of P2X7 receptor: a comprehensive review of its role in neurodegenerative disorders
• Unraveling mitochondrial dysfunction: comprehensive perspectives on its impact on neurodegenerative diseases
• User expectations and experiences of an assistive robotic arm in amyotrophic lateral sclerosis: a multicenter observational study
• Utility of the Repetitive Nerve Stimulation Test and Needle EMG in the Trapezius Muscle for the Early Diagnosis of ALS
• VAP-mediated membrane-tethering mechanisms implicate ER-PM contact function in pH homeostasis
• VPS35 or retromer as a potential target for neurodegenerative disorders: barriers to progress