Disease: Acromicric dysplasia
- <em>O-</em>Fucosylation of ADAMTSL2 is required for secretion and is impacted by geleophysic dysplasia-causing mutations
- A chinese boy with geleophysic dysplasia caused by compound heterozygous mutations in ADAMTSL2
- A Japanese child with geleophysic dysplasia caused by a novel mutation of FBN1
- A report of three families with FBN1-related acromelic dysplasias and review of literature for genotype-phenotype correlation in geleophysic dysplasia
- A Review of Three Chinese Cases of Acromicric/Geleophysic Dysplasia with FBN1 Mutations
- Accommodative esotropia and Brown syndrome in a girl with recessive geleophysic dysplasia
- Acromelic dysplasias: how rare musculoskeletal disorders reveal biological functions of extracellular matrix proteins
- Acromicric dysplasia
- Acromicric dysplasia
- Acromicric dysplasia and geleophysic dysplasia: similarities and differences
- Acromicric dysplasia caused by a mutation of fibrillin 1 in a family: A case report
- Acromicric Dysplasia Caused by a Novel Heterozygous Mutation of FBN1 and Effects of Growth Hormone Treatment
- Acromicric dysplasia due to a novel missense mutation in the fibrillin 1 gene in a three-generation family
- Acromicric dysplasia with stiff skin syndrome-like severe cutaneous presentation in an 8-year-old boy with a missense FBN1 mutation: Case report and literature review
- Acromicric dysplasia: long term outcome and evidence of autosomal dominant inheritance
- ADAMTS proteins as modulators of microfibril formation and function
- Adamtsl2 deletion results in bronchial fibrillin microfibril accumulation and bronchial epithelial dysplasia--a novel mouse model providing insights into geleophysic dysplasia
- ADAMTSL2 mutations determine the phenotypic severity in geleophysic dysplasia
- Bilateral carpal tunnel syndrome in a 9-year-old boy with acromicric dysplasia
- Cardiac involvement in geleophysic dysplasia in three siblings of a Saudi family
- Case Report: Two different acromelic dysplasia phenotypes in a Chinese family caused by a missense mutation in <em>FBN1</em> and a literature review
- Children with short-limbed short stature in pediatric endocrinological services in Japan
- Clinical manifestations and genetic analysis of 4 patients with variants of FBN1 gene
- Clinical phenotype and genetic analysis of six Chinese patients affected with Acromicric dysplasia due to variants of FBN1 gene
- Clinical Phenotype of Musladin-Lueke Syndrome in 2 Beagles
- Cooperative Mechanism of ADAMTS/ ADAMTSL and Fibrillin-1 in the Marfan Syndrome and Acromelic Dysplasias
- Dental characteristics of patients with four different types of skeletal dysplasias
- Fibrillin protein pleiotropy: Acromelic dysplasias
- Fibrillin-1 mutations causing Weill-Marchesani syndrome and acromicric and geleophysic dysplasias disrupt heparan sulfate interactions
- From tall to short: the role of TGFβ signaling in growth and its disorders
- Geleophysic and acromicric dysplasias: natural history, genotype-phenotype correlations, and management guidelines from 38 cases
- Geleophysic dysplasia associated with bilateral angle closure glaucoma
- Geleophysic dysplasia--acromicric dysplasia with evidence of glycoprotein storage
- Geleophysic dysplasia, unilateral choroidal folds and myelinated nerve fiber layer: A case report
- Geleophysic dysplasia: 48 year clinical update with emphasis on cardiac care
- Geleophysic dysplasia: a novel in-frame deletion of a tandem repeat in the ADAMTSL2 gene
- Genetic and molecular aspects of acromelic dysplasia
- Genotype-phenotype correlation and expansion of orodental anomalies in LTBP3-related disorders
- Immunolocalisation of fibrillin microfibrils in the calf metacarpal and vertebral growth plate
- Juvenile idiopathic arthritis, mitral valve prolapse and a familial variant involving the integrin-binding fragment of FBN1
- Leri's pleonosteosis, a congenital rheumatic disease, results from microduplication at 8q22.1 encompassing GDF6 and SDC2 and provides insight into systemic sclerosis pathogenesis
- Limb- and tendon-specific Adamtsl2 deletion identifies a role for ADAMTSL2 in tendon growth in a mouse model for geleophysic dysplasia
- Missense mutations in FBN1 exons 41 and 42 cause Weill-Marchesani syndrome with thoracic aortic disease and Marfan syndrome
- Molecular screening of ADAMTSL2 gene in 33 patients reveals the genetic heterogeneity of geleophysic dysplasia
- Moore-Federman syndrome and acromicric dysplasia: are they the same entity?
- More than meets the eye: The evolving phenotype of Weill-Marchesani syndrome-diagnostic confusion with geleophysic dysplasia
- Mutations in LTBP3 cause acromicric dysplasia and geleophysic dysplasia
- Mutations in the TGFβ binding-protein-like domain 5 of FBN1 are responsible for acromicric and geleophysic dysplasias
- Novel ADAMTSL2-mutations in a patient with geleophysic dysplasia type I
- Novel mutations in ADAMTSL2 gene underlying geleophysic dysplasia in families from United Arab Emirates
- Novel mutations in geleophysic dysplasia type 1
- Optic disc swelling in acromicric and geleophysic dysplasia
- Orthopedics management of acromicric dysplasia: follow up of nine patients
- Partial metaphyseal dysostosis of the acral or acromicric type
- Pathogenic variants affecting the TB5 domain of the fibrillin-1 protein: not only in geleophysic/acromicric dysplasias but also in Marfan syndrome
- Rapidly progressive mitral valve stenosis in patients with acromelic dysplasia
- Similarity of geleophysic dysplasia and Weill-Marchesani syndrome
- Skeletal manifestations of Marfan syndrome associated to heterozygous R2726W FBN1 variant: sibling case report and literature review
- Skin fibroblasts of patients with geleophysic dysplasia due to FBN1 mutations have lysosomal inclusions and losartan improves their microfibril deposition defect
- Sleep-disordered breathing and its management in children with rare skeletal dysplasias
- Subglottic stenosis in short-statured children: a case for further investigation of airway symptoms in patients with skeletal dysplasias
- The "Fantasy Island" syndrome. Identification of a new osteochondrodysplasia probably of autosomal dominant type
- The critical role of the TB5 domain of fibrillin-1 in endochondral ossification
- The fibrillin microfibril/elastic fibre network: A critical extracellular supramolecular scaffold to balance skin homoeostasis
- Three cases of Japanese acromicric/geleophysic dysplasia with FBN1 mutations: a comparison of clinical and radiological features
- Three novel mutations of the FBN1 gene in Chinese children with acromelic dysplasia
- Two Patients with Severe Short Stature due to a FBN1 Mutation (p.Ala1728Val) with a Mild Form of Acromicric Dysplasia