Vohwinkel syndrome
Overview
A rare condition where tight bands of thickened skin form around the base of fingers and toes and generally leads to self-amputation of the digit. Hearing loss is also associated with the condition.
Symptoms
* Skin lesions * Palmoplantar keratoderma * Constrictions of the fingers * Constrictions of the toes * Hyperkeratotic plaques of the hands
Causes
1. Conductivehearing loss 1. Externalauditory canal disorders 1. Atresia of external auditory canal 2. Impacted cerumen 3. Otitis externa 4. Exostosis 5. Masses 2. Middle ear disorders 1. Acuteand chronic otitis media 2. Otitis media with effusion 3. Tympanic membrane perforation 4. Hemotympanum 5. Tympanosclerosis 6. Ossicular chain defect, disruption,or fixation 7. Cholesteatoma and other middle earmasses 2. Sensorineural hearing loss 1. Sensorineuralhearing loss without associated abnormalities 2. Sensorineural hearing loss with associatedabnormalities 3. Chromosomal disorders 4. Inner ear malformations 1. Labyrinthineaplasia 2. Common cavity malformation 3. Cochlear malformations 4. Large vestibular aqueduct 5. Prematurity 6. Hypoxic-ischemic encephalopathy 7. Bilirubin encephalopathy (kernicterus) 8. Infection 9. Trauma 10. Drugs 11. Perilymph fistula 12. Neoplasm 13. Ménière disease 14. Unknown 3. Mixed hearing loss
Diagnosis
The signs and symptom information on this page attempts to provide a list of some possible signs and symptoms of Vohwinkel syndrome. This medical information about signs and symptoms for Vohwinkel syndrome has been gathered from various sources, may not be fully accurate, and may not be the full list of Vohwinkel syndrome signs or Vohwinkel syndrome symptoms. Furthermore, signs and symptoms of Vohwinkel syndrome may vary on an individual basis for each patient. Only your doctor can provide adequate diagnosis of any signs or symptoms and whether they are indeed Vohwinkel syndrome symptoms.