Sternal malformation vascular dysplasia associatio

Overview

Sternal malformation vascular dysplasia association: A rare disorder characterized by a cleft of the sternum and facial hemangiomata.

Symptoms

* Sternum cleft * Atrophic skin along sternum cleft * Facial skin hemangiomata * Small bowel mucosa hemangiomata * Partial sternal cleft * Complete sternal cleft * Absent pericardium anteriorly * Unilateral cleft lip * Small lower jaw * Glossoptosis