Hydroa vacciniforme- familial
Overview
A rare skin disorder characterized the development of crusting skin eruptions following exposure to the sun.
Symptoms
- Malaise - Hyperthermia - Restlessness - Itching - Skin eruption
Treatment
Medical Care: In addition to medication and certain restrictions on activity, management may include a prophylactic "hardening" course of phototherapy. * Low-dose, narrow-band UV-B (TL-01) phototherapy, either daily or 3 times a week in the spring, may confer relative photoprotection.13 * Psoralen photochemotherapy (PUVA) administered prophylactically in older patients may be effective in desensitization. Consultations: * Consult a dermatologist for evaluation and management of HV. * Consult an ophthalmologist for evaluation and management of associated eye findings. Diet: Generally, no diet restrictions or requirements are indicated in the management of HV. Activity: Strict sun avoidance, appropriate clothing, and frequent application of high sun protection factor (SPF) sunscreens with UV-A blocking agents are advised.