Camurati Engelmann disease- type 2
Camurati-Engelmann Disease (CED) is a form of dysplasia and a very rare autosomal dominant genetic disorder that causes characteristic anomalies in the skeleton. Patients typically have heavily-thickened bones, especially along the shafts of the long bones (called diaphyseal dysplasia). The skull bones may be thickened so that the passages through the skull that carry nerves and blood vessels become narrowed, sometimes leading to sensory deficits such as blindness, or deafness.
