Multiple endocrine neoplasia- type 2B
Multiple endocrine neoplasia (MEN) syndromes are mostly inherited conditions in which several endocrine glands develop benign (non-cancerous) or malignant (cancerous) tumours or hyperplasia (grow excessively without forming tumours). There are 2 main types of MEN, MEN type 1 and MEN type 2. MEN type 2 is further split into 3 subtypes: * MEN type 2A * FMTC (familial medullary thyroid carcinoma) * MEN type 2B (formerly known as MEN type 3). Multiple endocrine neoplasia type 2B disease has additional features including mucosal neuromas (nerve tumours on the mucous membranes), neuromas in the gut that lead to gastrointestinal abnormalities, and striking facial appearance associated with Marfanoid habitus (slender, tall, long fingers & toes, and high arched palate). These features may be the first sign of an internal malignancy and should prompt further investigation.
