IBIDS syndrome
Overview
BIDS syndrome: A rare inherited skin disorder characterized by red, dry, scaly skin (I - ichthyosis), brittle hair (B), impaired physical and mental development (I), decreased fertility (D) and short stature (S). It is the same as PIBIDS syndrome but doesn't involve photosensitivity.
Symptoms
The list of signs and symptoms mentioned in various sources for IBIDS syndrome includes the 29 symptoms listed below: Birth Fine, dark skin scales Retarded growth Mental retardation Lack of subcutaneous fat Short hair Brittle hair Dysplastic nails Congenital cataracts Spasticity Impaired ability to control voluntary movements Decreased fertility Dry scaly skin Sulfur deficiency in hair Sparse hair Delayed physical development Red skin Prematurely aged appearance Beaked nose Receding chin Protruding ears Low birth weight Short stature Neurosensory deafness Seizures Tremors Undescended testes Underdeveloped female genitalia Absence of female breast tissue Note that IBIDS syndrome symptoms usually refers to various symptoms known to a patient, but the phrase IBIDS syndrome signs may refer to those signs only noticable by a doctor
Causes
Bowen’s disease Bowen’s disease is a common form of intraepidermal carcinoma that causes painless, erythematous plaques that are raised and indurated with a thick, hyperkeratotic scale and, possibly, ulcerated centers. TopDermatitis Exfoliative dermatitis begins with rapidly developing generalized erythema. Desquamation with fine scales or thick sheets of all or most of the skin surface may cause life-threatening hypothermia. Other possible complications include cardiac output failure and septicemia. Systemic signs and symptoms include a low-grade fever, chills, malaise, lymphadenopathy, and gynecomastia. With nummular dermatitis, round, pustular lesions commonly ooze purulent exudate, itch severely, and rapidly become encrusted and scaly. Lesions appear on the extensor surfaces of the limbs, posterior trunk, and buttocks. Seborrheic dermatitis begins with erythematous, scaly papules that progress to larger, dry or moist, greasy scales with yellowish crusts. This disorder primarily involves the center of the face, the chest and scalp and, possibly, the genitalia, axillae, and perianal regions. Pruritus occurs with scaling. TopDermatophytosis Tinea capitis produces lesions with reddened, slightly elevated borders and a central area of dense scaling; these lesions may become inflamed and pus-filled (kerions). Patchy alopecia and itching may also occur. Tinea pedis causes scaling and blisters between the toes. The squamous type produces diffuse, fine, branlike scales. Adherent and silvery white, they’re most prominent in skin creases and may affect the entire dorsum of the foot. Tinea corporis produces crusty lesions. As they enlarge, their centers heal, causing the classic ringworm shape.
Prevention
The 'prognosis' of IBIDS syndrome usually refers to the likely outcome of IBIDS syndrome. The prognosis of IBIDS syndrome may include the duration of IBIDS syndrome, chances of complications of IBIDS syndrome, probable outcomes, prospects for recovery, recovery period for IBIDS syndrome, survival rates, death rates, and other outcome possibilities in the overall prognosis of IBIDS syndrome. Naturally, such forecast issues are by their nature unpredictable