Hypothalamic hamartomas
Overview
Hypothalamic hamartoma (abbreviated as HH) is a congenital condition consisting of a mass of disorganized neuronal or glial tissue on or near the hypothalamus. HH is generally not detected on CT scans, and on MRI it is isointense to gray matter. The size of HHs varies from less than 1 cm to more than 3 cm.
Prognosis
Surgery is often effective in eliminating the seizures, behavior problems, and endocrine disturbances. For individuals who are not candidates for surgery, life-long treatment with medication typically is required
Treatment
If the hamartoma extends beyond the hypothalamus and below the brain, treatment with surgery may be an option. Seizure medicines can also be beneficial, as well as medications aimed at hormonal and behavioral problems, if needed.