Multicystic renal dysplasia- bilateral
Overview
A rare congenital disorder where multiple cysts develop in the kidneys which affects their ability to function normally. The condition is results in death prior to or within weeks of birth.
Symptoms
* Kidney dysfunction * Abdominal mass * Enlarged kidneys * Reduced amniotic fluid * Pulmonary hypoplasia * Potter facies
Causes
Almost any type of obstructive uropathy can result in hydronephrosis. The most common causes are benign prostatic hyperplasia, urethral strictures, and calculi; less common causes include strictures or stenosis of the ureter or bladder outlet, congenital abnormalities, abdominal tumors, blood clots, and neurogenic bladder. If obstruction is in the urethra or bladder, hydronephrosis is usually bilateral; if obstruction is in a ureter, it’s usually unilateral. Obstructions distal to the bladder cause the bladder to dilate and act as a buffer zone, delaying hydronephrosis. Total obstruction of urine flow with dilation of the collecting system ultimately causes complete cortical atrophy and cessation of glomerular filtration. Hydronephrosis occurs in 1 out of every 100 people.
Diagnosis
* Bladder & Urinary Health: Home Testing: o Home Bladder Tests o Home Urinary Tract Infection (UTI) Tests o Home Cystitis Tests o Home Kidney Tests o Home Urine Protein Tests (Kidney Function) o Home Prostate Cancer Tests * Kidney Health: Home Testing: o Home Microalbumin Tests (Kidney) o Home Urine Protein Tests (Kidney) o Home Urinary Tract Infection (UTI) Tests
Treatment
The goals of treatment are to preserve renal function and prevent infection through surgical removal of the obstruction, such as dilation for stricture of the urethra or prostatectomy for benign prostatic hyperplasia. If renal function has already been affected, therapy may include a diet low in protein, sodium, and potassium. This diet is designed to stop the progression of renal failure before surgery. Inoperable obstructions may necessitate decompression and drainage of the kidney using a nephrostomy tube placed temporarily or permanently in the renal pelvis or placement of a ureteral stent to allow the ureter to drain. Concurrent infection requires appropriate antibiotic therapy .